Diagnosis and therapy of children hemophagocytic lymphohistiocytosis
10.3760/cma.j.issn.1673-4408.2021.06.010
- VernacularTitle:儿童噬血性淋巴组织细胞增生症的诊断和治疗进展
- Author:
Lu WANG
1
;
Yubin WU
Author Information
1. 中国医科大学附属盛京医院小儿肾脏风湿免疫科,沈阳 110004
- Keywords:
Children;
Hemophagocytic lymphohistiocytosis;
Pathogenesis;
Diagnosis;
Treatment
- From:
International Journal of Pediatrics
2021;48(6):405-409
- CountryChina
- Language:Chinese
-
Abstract:
Hemophagocytic lymphohistiocytosis(HLH)is a life-threatening inflammatory response syndrome, which progresses rapidly.Its etiology and clinical manifestations are diverse, and its diagnosis is difficult, and the rescue treatment has not been unified at home and abrord.The paper reviews the classification, pathogenesis, clinical manifestations, laboratory indexs, diagnosis and treatment of HLH, in order to provide reference for timely diagnosis and individualized treatment.