Severe juvenile dermatomyositis
10.3760/cma.j.issn.1673-4912.2020.05.005
- VernacularTitle:幼年重症皮肌炎
- Author:
Xuemei TANG
1
Author Information
1. 重庆医科大学附属儿童医院风湿免疫科 儿童发育疾病研究教育部重点实验室 国家儿童健康与疾病临床医学研究中心 儿童发育重大疾病国家国际科技合作基地 儿童感染免疫重庆市重点实验室 400014
- From:
Chinese Pediatric Emergency Medicine
2020;27(5):341-345
- CountryChina
- Language:Chinese
-
Abstract:
Juvenile dermatomyositis(JDM)is a common autoimmune inflammatory myopathy in childhood.The manifestations are specific skin lesions, chronic muscular inflammation and systemic vasculitis.The treatment was mainly glucocorticoid combined with immunosuppressive agents, the overall prognosis of JDM was better than that of adults.The key to improve the prognosis of patients is to make identification and management of severe cases.This paper introduced the clinical characteristics of severe JDM, myositis specific antibody and pulmonary imaging changes, focusing on the clinical characteristics of pulmonary lesions, examinations and treatment strategies, in order to improve the recognition and diagnosis of severe JDM.
