The advance on the prenatal diagnosis and management of fetal long QT syndrome
10. 3760/cma. j. issn. 2095-428x. 2019. 04. 020
- VernacularTitle:胎儿长QT间期综合征的产前诊治和管理进展
- Author:
Shuran SHAO
1
;
Kaiyu ZHOU
;
Yimin HUA
Author Information
1. 四川大学华西第二医院儿科
- Keywords:
Long QT syndrome;
Malignant arrhythmia;
Fetus;
Diagnosis;
Treatment;
Management
- From:
Chinese Journal of Applied Clinical Pediatrics
2019;34(4):317-320
- CountryChina
- Language:Chinese
-
Abstract:
Long QT syndrome(LQTS)is a rare and inherited cardiac channelopathy with high lethality,which is characterized by prolonged QTc interval and frequent malignant arrhythmia,the cause of the disease is that mutations of genes coding for cardiac ion channel subunit or channel associated proteins. Since some fetal LQTS may die in utero or neonatal period,thus,prenatal suspicion or diagnosis of fetal LQTS may improve their outcome and prognosis. There-fore,this review prepares to discuss around the prenatal diagnosis and management of fetal LQTS.