Surgical treatment of aortic root aneurysm in adolescent patients with Marfan syndrome
10.7507/1007-4848.201709069
- VernacularTitle:马方综合征少年儿童主动脉根部瘤的外科治疗
- Author:
XIA Yu
1
;
LI Chengnan
1
;
GE Yipeng
1
;
YANG Yi
1
;
CHEN Lei
1
;
ZHU Junming
1
;
LIU Yongmin
1
;
SUN Lizhong
1
Author Information
1. Department of Cardiac Surgery, Beijing Anzhen Hospital, Capital Medical University, Beijing Institute of Heart, Lung and Blood Vessel Diseases, Beijing, 100029, P.R.China
- Publication Type:Journal Article
- Keywords:
Marfan syndrome;
adolescent/teenage;
aortic root aneurysm;
Bentall procedure
- From:
Chinese Journal of Clinical Thoracic and Cardiovascular Surgery
2018;25(9):777-780
- CountryChina
- Language:Chinese
-
Abstract:
Objective To study the mid-term and long-term postoperative results of Bentall procedure in patients with Marfan syndrome. Methods From February 2009 to July 2016, ten adolescent patients (mean age of 12.30±2.31 years ranged 9-16 years, mean height of 172.50±12.55 mm, mean weight of 48.60±17.08 kg) underwent Bentall procedure in our hospital. All these teenage patients were with Marfan syndrome, 6 boys and 4 girls. Five of them underwent mitral valve replacement procedure at the same time while 2 of them with tricuspid valvuloplasty. Results No mortality was found in hospitalization. One patient suffered respiratory failure after surgery. No renal failure, mediastinal infection or re-operation caused by bleeding were observed. All were well followed up for 62 months. One died of malignant arrhythmia, the other were in good condition with the latest interview. Conclusion Teenage patients with Marfan syndrome who underwent Bentall procedure have favorable outcomes in mid-term and long-term follow-up, they probably will not suffer anti-coagulation complications and restriction of growth
