Pediatric pulmonary alveolar proteinosis
10.3760/cma.j.issn.2095-428X.2018.04.020
- VernacularTitle:儿童肺泡蛋白沉积症
- Author:
Wei XU
1
;
Kunling SHEN
Author Information
1. 首都医科大学附属北京儿童医院过敏反应科
- Keywords:
Pulmonary alveolar proteinosis;
Child;
Whole lung lavage
- From:
Chinese Journal of Applied Clinical Pediatrics
2018;33(4):317-320
- CountryChina
- Language:Chinese
-
Abstract:
Pulmonary alveolar proteinosis is a rare disease in children.The accumulation of massive amount of lipid and protein in the alveolar can lead to the progressive dyspnea and hypoxemia.The diagnosis could be made with the high resolution computed tomography and pathological findings.Appropriate treatments according to the pathogenesis,together with whole lung lavage,can significantly improve disease outcome.This article will provide a review of the pathogenesis,clinical features,therapeutic approach and disease prognosis of pediatric pulmonary alveolar proteinosis.
