Paroxysmal Nocturnal Hemoglobinuria Presenting as Recurrent Jejunitis.
10.3904/kjm.2016.90.2.132
- Author:
Ji Won KIM
1
;
Jun Young KIM
;
Jin Hae KIM
;
Hye In KIM
;
Young Nam KIM
;
Young Ho KIM
;
Sung Noh HONG
Author Information
1. Department of Medicine, Samsung Medical Center, Sungkyunkwan University School of Medicine, Seoul, Korea. gisnhong@gmail.com
- Publication Type:Case Report
- Keywords:
Jejunitis;
Paroxysmal nocturnal hemoglobinuria;
Thrombosis;
Small bowel ischemia
- MeSH:
Adult;
Bone Marrow;
Diagnosis, Differential;
Hematopoietic Stem Cells;
Hemoglobinuria;
Hemoglobinuria, Paroxysmal*;
Hemolysis;
Humans;
Ischemia;
Thrombosis
- From:Korean Journal of Medicine
2016;90(2):132-135
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Paroxysmal nocturnal hemoglobinuria (PNH) is a rare acquired hematopoietic stem cell disorder characterized by chronic complement-mediated intravascular hemolysis, nocturnal hemoglobinuria, predisposition to thrombosis and secondary bone marrow failure. Small bowel ischemia is a complication of PNH but has not been reported to date in a Korean adult. We report here a case of PNH presenting as recurrent jejunitis. Despite the uncommon etiology, PNH should be considered in the differential diagnosis of patients with unexplained recurrent jejunitis.
