Surgical Treatment of Two Cases of Benign Symmetrical Lipomatosis Causing Dyspnea.
- Author:
Soon Ho KWON
1
;
Sang Cheol KIM
;
Hyung Seok SEO
;
Hong Shik CHOI
Author Information
1. Department of Otorhinolaryngology, The Institute of Logopedics and Phoniatrics, Yonsei University College of Medicine, Seoul, Korea. hschoi@yumc.yonsei.ac.kr
- Publication Type:Case Report
- Keywords:
Madelung's disease;
Lipomatosis;
multiple symmetrical;
Dyspnea
- MeSH:
Dyspnea*;
Humans;
Laryngoscopes;
Lipomatosis*;
Lipomatosis, Multiple Symmetrical;
Lower Extremity;
Middle Aged;
Neck;
Rare Diseases;
Shoulder;
Tomography, X-Ray Computed;
Upper Extremity
- From:Korean Journal of Otolaryngology - Head and Neck Surgery
2006;49(7):758-762
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Benign symmetrical lipomatosis, known as Madelung's disease, is a rare disease characterized by non-encapsulated fat tissue accumulation in a symmetrical manner around the neck, shoulders, and upper extremities, rarely involving the lower limbs and the lower body. To date, there have been approximately 200 cases reported. We experienced two cases of Madelung's disease, 57 and 59 year-old man with neck and shoulder swelling and the symptom of dyspnea. Laryngoscopic and CT scan findings showed severe narrowing of supraglottic and paraglottic area, caused by fat tissue accumulation. The fat tissues were surgically excised, one by external approach and the other by laryngomicrosurgery using LASER under direct laryngoscope, with successful result. We report it with a review of the current literatures.
