A Case of Malignant Peripheral Nerve Sheath Tumor on Paranasal Sinus.
- Author:
Hyun Jik KIM
1
;
Jin Young KIM
;
Chang Hoon KIM
;
Joo Heon YOON
Author Information
1. Department of Otorhinolaryngology, Yonsei University College of Medicine, Seoul, Korea. jhyoon@yumc.yonsei.ac.kr
- Publication Type:Case Report
- Keywords:
Peripheral nerve sheath tumor;
Malignant;
Paranasal sinus neoplasm
- MeSH:
Abdomen;
Extremities;
Head;
Nasal Cavity;
Neck;
Neurilemmoma;
Neurofibromatosis 1;
Paranasal Sinus Neoplasms;
Paranasal Sinuses;
Peripheral Nerves*;
Rare Diseases;
Thorax
- From:Korean Journal of Otolaryngology - Head and Neck Surgery
2005;48(2):263-266
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Malignant peripheral nerve sheath tumor, a highly aggressive neoplasm of nerve sheath origin (also known as malignant schwannoma, malignant neurilemoma), is an uncommon entity that may occasionally occur in the head and neck. In the majority of cases, malignant peripheral nerve sheath tumors are found in the extremities, followed by the occurrence in the paravertebral region of the thorax and abdomen. The head and neck are involved in less than 10% of cases, which is especially true in rare diseases of the nasal cavity and paranasal sinuses. We present a case of malignant peripheral nerve sheath tumor of the paranasal sinus without a definite evidence of von Recklinghausen's disease or benign preexisting peripheral nerve sheath tumor with a review of literatures.
