Adult Sturge-Weber syndrome without facial hemangioma: report of one case.
- Author:
Rong ZHANG
1
;
Wei CHEN
2
;
Qiang HU
3
;
Sudeep SHRESTHA
3
Author Information
1. Department of Ophthalmology, Shaoxing Peoples Hospital, Shaoxing 312000, China;College of Optometry, Wenzhou Medical University, Wenzhou 325027, China.
2. Department of Ophthalmology, Shaoxing Peoples Hospital, Shaoxing 312000, China
3. Department of Neurosurgery, Second Affiliated Hospital, Zhejiang University School of Medicine, Hangzhou 310009, China.
- Publication Type:Case Reports
- MeSH:
Adult;
Angiography;
Anticonvulsants;
therapeutic use;
Brain;
pathology;
Epilepsy;
Humans;
Magnetic Resonance Imaging;
Male;
Middle Aged;
Seizures;
drug therapy;
Sturge-Weber Syndrome;
pathology
- From:
Journal of Zhejiang University. Medical sciences
2014;43(5):588-590
- CountryChina
- Language:Chinese
-
Abstract:
Sturge-Weber syndrome (SWS) is characterized by angiomas affecting the ophthalmic division of the trigeminal nerve, epilepsy, intellectual impairment, hemiplegia and glaucoma. We report a patient who developed SWS without facial hemangioma (SWS type III) in his adulthood. The patient presented with repeated episodes of headache since age 37 year. He manifested first attack of seizure at the age 47 year followed by aphasia and right upper limb palsy. Brain CT scan revealed right parietal-occipital calcification, brain CT angiography showed right temporal lobe and occipital lobe vascular malformation, and MRI showed leptomeningeal enhancement in the riht cerebral piamater. The seizure was controlled with antiepileptic drugs and reviewed in routine follow up.
