Anesthetic Management of a Patient with a Single Ventricle and Pheochromocytoma: A case report.
10.4097/kjae.2004.47.4.590
- Author:
Yang Hyun KIM
1
;
Ah Young OH
;
Chong Sung KIM
Author Information
1. Department of Anesthesiology and Pain Medicine, Seoul National University College of Medicine, Seoul, Korea. kimcs@snu.ac.kr
- Publication Type:Case Report
- Keywords:
anesthesia;
pheochromocytoma;
single ventricle;
surgery
- MeSH:
Anesthesia;
Anoxia;
Female;
Fontan Procedure;
Heart Defects, Congenital;
Humans;
Parturition;
Pheochromocytoma*;
Prognosis;
Young Adult
- From:Korean Journal of Anesthesiology
2004;47(4):590-592
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Single ventricle is a rare congenital anomaly that accounts for about 1.5% of all congenital heart defects at birth. It is believed to carry a poor prognosis when untreated, which has led to a more aggressive surgical approach in childhood. The surgical approach is an initial palliative operation in the form of a shunt, followed by a Fontan operation or one of its modifications. However, a few case reports have noted the survival of patients to the fifth or sixth decade without surgical repair. We experienced an anesthesia of a 20-year-old female patient for excision of the pheochromocytoma who had chronic hypoxia due to partially corrected single ventricle anomaly. We report this experience with brief review of literature.