Noninvasive Positive Pressure Ventilation Using a Face Mask for a Child with Spinal Muscular Atrophy: A case report.
10.4097/kjae.2004.46.4.480
- Author:
Jung Yeon YUN
1
;
Chong Sung KIM
Author Information
1. Department of Anesthesiology and Pain Medicine, Seoul National University College of Medicine, Seoul, Korea.
- Publication Type:Case Report
- Keywords:
mask;
neuromuscular disease;
noninvasive positive pressure ventilation;
pediatric
- MeSH:
Adult;
Carbon Dioxide;
Child*;
Humans;
Hypoventilation;
Intensive Care Units;
Intubation;
Masks*;
Mortality;
Muscular Atrophy, Spinal*;
Neuromuscular Diseases;
Oxygen;
Positive-Pressure Respiration*;
Quality of Life;
Respiration;
Respiratory Insufficiency;
Ventilation
- From:Korean Journal of Anesthesiology
2004;46(4):480-483
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Respiratory complications are a major cause of morbidity and mortality in pediatric neuromuscular disease. In adults with acute or chronic respiratory failure, noninvasive positive pressure ventilation (NIPPV) is superior to standard therapy in terms of preventing intubation and reducing mortality. Moreover, domiciliary ventilation with NIPPV in children can prolong life and optimize the quality of life by allowing patients to eat, speak and sleep well. But the role of NIPPV in pediatric patients with respiratory failure is not well established. We report the case of a pediatric spinal muscular atrophy patient who was managed by using NIPPV for acute hypercapnic respiratory failure at a pediatric intensive care unit and by nocturnal hypoventilation late r at home. In this case, NIPPV restored normal blood oxygenation, removed excess blood carbon dioxide, and normalized the work and pattern of breathing.
