A case of simple type Caroli's disease confined to one segment of the liver.
- Author:
Sung Jae YOO
1
;
Young Soo MOON
;
Sang Won LEE
;
Jeon Ho YANG
;
Sang Jae PARK
;
Joong Won PARK
;
Chang Min KIM
Author Information
1. Center for Liver Cancer, National Cancer Center, Gyeonggi, Korea.
- Publication Type:Case Report
- Keywords:
Caroli disease;
Bile duct disease;
Intrahepatic choledochal cyst
- MeSH:
Abdominal Pain;
Bile Duct Diseases;
Bile Ducts;
Biliary Tract;
Caroli Disease*;
Cholangitis;
Choledochal Cyst;
Dilatation;
Drainage;
Female;
Fibrosis;
Humans;
Hypertension, Portal;
Liver*;
Magnetic Resonance Imaging;
Mastectomy, Segmental;
Ultrasonography;
Young Adult
- From:Korean Journal of Medicine
2005;68(4):448-452
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Caroli's disease is a rare congenital anomaly of the intrahepatic biliary tree characterized by multiple, saccular and cystic dilatation of the bile ducts that are connected with the biliary drainage system. It is frequently associated with congenital hepatic fibrosis, resulting in portal hypertension. The complications are stone formation, recurrent cholangitis and occasionally cancer. Less than 20% of all cases reported describe monolobar or segmental invovement. In the pure form or simple type, the patient presents without hepatic fibrosis or portal hypertension. We report a case of simple type Caroli's disease confined to the one hepatic segment in a 22 year-old woman. She was admitted because of cystic mass, associated with right upper abdominal pain. Radiologic findings including abdominal ultrasonography, computerized tomography, magnetic resonance imaging demonstrated that the cystic lesions involving segment VIII of the liver. The lesion was treated with hepatic segmentectomy.
