Osteopetrosis tarda.
- Author:
Young Hee KIM
1
;
Jae Seo YI
;
Suk Ja YOON
;
Byung Cheol KANG
Author Information
- Publication Type:Original Article
- Keywords: hereditary bone disorder; Growth disorder; Tooth eruption
- MeSH: Anemia; Blindness; Bone Density; Child; Deafness; Dental Clinics; Dentists; Diagnosis; Facial Bones; Growth Disorders; Humans; Intellectual Disability; Jaw; Male; Mastoid; Osteomyelitis; Osteopetrosis*; Paranasal Sinuses; Skull; Skull Base; Thrombocytopenia; Tooth; Tooth Eruption; Tooth, Deciduous; X-Ray Film
- From:Journal of Korean Academy of Oral and Maxillofacial Radiology 1999;29(2):507-521
- CountryRepublic of Korea
- Language:Korean
- Abstract: Osteopetrosis is an uncommon hereditary bone disorder whose prominent radiologic feature characterized by increased bone density. The authors reported a 7-year-old male patient who referred from local dental clinic for dental problems such as early exfoliation of deciduous teeth(#54,73,83) and delayed eruption of permanent teeth(#31,41,36,46). The patient appeared as a poorly developed. Dental X-ray films showed early exfoliation of deciduous teeth, delayed eruption of permanent teeth, and rampant caries. Lateral view of skull demonstrated increased opacity of calvarium, facial bones, and skull base. Generally the skeletal density is greatly increased throughout all bones. Facial CT showed poor development of paranasal sinuses and mastoid air cells. No hematopoietic and neurologic complications such as anemia, thrombocytopenia, blindness and deafness were found. Also mental retardation was not found. The final diagnosis of this case was a osteopetrosis tarda. Sometimes patient with osteopetrosis tarda may be developed dental problems prior to severe systemic symptoms. The dentist can be the first clinician to see the patient. It is very important for the dentist to have the knowledge of the osteopetrosis and to care the patient's dental problems to prevent complication such as osteomyelitis of jaws.
