INTRODUCTION: We report a 17-month old girl with a congenital erythematous papule with fine tuft of hair over her lumbosacral area that later developed multiple intraspinal abscesses involving the whole length of her spinal cord as well as tethered cord and dermal sinus at the level of L3-L4 seen on spinal magnetic resonance imaging (MRI). CLINICAL PRESENTATION: She presented with gross motor delay, and then had yellowish discharge draining from her dermal sinus at 10 months of age treated with an oral antibiotic. The yellowish discharge recurred at 17 months of age associated with intermittent fever, progressive paraplegia, flaccidity, areflexia of her lower limbs and urinary and stool retention. DIAGNOSTIC WORK-UP: She underwent spinal cord MRl aside from the laboratory examinations that included complete blood count, urinalysis, blood culture and sensitivity, wound discharge culture and sensitivity and coagulation profile. TREATMENT AND FOLLOW-UP: The patient was given ceftriaxone, vancomycin and oxacillin preoperatively. She underwent laminectomy, excision of dermal sinus tract and drainage of pus. Postoperatively, she was maintained on meropenem for 6 weeks and continued physical therapy as an outpatient basis.