FAMILIAL FORM OF CRANIOFACIAL FIBROUS DYSPLASIA: A CASE REPOR
- Author:
Ayat GAMAL-ABDELNASER
1
;
Noha Adel AZAB
2
;
Soha MOHIEELDIN
3
;
Tarek EL-GHAREEB
4
Author Information
1. Department of Oral Medicine and Periodontology, Faculty of Dentistry, Ahram Canadian University, Egypt
2. Department of Oral Medicine and Periodontology, Faculty of Dentistry, Cairo University, Egypt
3. Department of Endodontics, Faculty of Oral and Dental Medicine, Ahram Canadian University, Egypt
4. Department of Oral and Maxillofacial Surgery, Faculty of Dentistry, Cairo University, Egypt
- Publication Type:Journal Article
- Keywords:
Craniofacial fibrous dysplasia;
Endodontic;
Esthetics;
Facial asymmetry;
GNAS1 protein;
Pulpitis
- From:
Brunei International Medical Journal
2022;18():94-98
- CountryBrunei Darussalam
- Language:English
-
Abstract:
Fibrous dysplasia is a benign disease of bone that may affect single or multiple bones. Craniofacial fibrous dysplasia may occur in a familial manner. This report deals with a patient who presented with multiple bony craniofacial prominences; with a positive family history of similar lesions. The lesions started to appear at his early teenage years and new lesions continued to arise and grow till 18 years of age. The lesions were expansile causing esthetic impairment. The case was diagnosed as a familial form of craniofacial fibrous dysplasia. Surgical recontouring was performed to the lesion that formed the patient's chief complaint. Later on the fibro-osseous lesion crept into the pulp canals of the related teeth causing pulpitis. Craniofacial fibrous dysplasia presentation varies according to the area affected, but it generally has a favorable diagnosis. However, we do recommend that periodic vitality testing be performed for teeth in proximity of the lesion.
- Full text:2026072314014080699BIMJ2022-18-94-98.pdf
