Alveolar Soft Part Sarcoma as a Great Masquerader of Unilateral Sinonasal Tumour in Child: A Case Report
https://doi.org/10.21315/aos2024.1902.CR01
- Author:
Shao Peng Tee
1
;
Shao Peng Tee
2
;
Nur Adillah Lamry
2
;
Hafiz Mohamad Mahbob
2
;
Intan Nurjannah Darwin
3
;
Irfan Mohamad
1
Author Information
1. Department of Otorhinolaryngology-Head and Neck Surgery, School of Medical Sciences, Health Campus, Universiti Sains Malaysia, 16150 Kubang Kerian, Kelantan, Malaysia
2. Department of Otorhinolaryngology-Head and Neck Surgery, Hospital Sultan Ismail, Jalan Mutiara Emas Utama, Taman Mount Austin, 81100 Johor Bahru, Johor, Malaysia
3. Department of Pathology, Hospital Sultanah Aminah, Jalan Persiaran Abu Bakar Sultan, 80100 Johor Bahru, Johor, Malaysia
- Publication Type:Case Reports
- Keywords:
Alveolar soft part;
chemoradiotherapy;
paediatric;
paranasal sinus;
sarcoma
- From:
Archives of Orofacial Sciences
2024;19(2):187-193
- CountryMalaysia
- Language:English
-
Abstract:
Alveolar Soft Part Sarcoma as a Great Masquerader of Unilateral Sinonasal Tumour in Child: A Case Report:Alveolar soft part sarcoma (ASPS) is a rare mesenchymal neoplasm that accounts for less than 1%
of all sarcoma and the most common site of tumour is found in the soft tissue of the extremity. The
incidence of ASPS in paediatric age group is rare. It is extremely uncommon for the tumour arising
from the sinonasal within the head and neck region. Most of the reported cases were in the orbit and
tongue. Localised ASPS carries a good prognosis after complete total resection. Diagnosing ASPS can
be challenging as it can be a masquerader to other sinonasal soft tissue malignancy which required
the laborious process of histopathological examination, immunohistochemistry, and ultrastructural
examination to solve the complexity. We encountered an 11-year-old girl who presented with sudden
onset of left nasal obstruction and on examination noted a unilateral vascular mass in the left nasal cavity turned out to be ASPS. She underwent left nasal tumour debulking via endoscopic approach under general anaesthesia. Post-operative, she recovered well with regular endoscopic surveillance and was referred to the oncology team for post-operative radiotherapy.
- Full text:2026060623222655755Alveolar Soft Part Sarcoma as a Great Masquerader.pdf
