A case of MRKH syndrome combined with adenomyosis without endometrium and literature review
10.3760/cma.j.cn101721-20241013-00328
- VernacularTitle:Mayer-Rokitansky-Küster-Hauser综合征合并无子宫内膜子宫腺肌病1例并文献复习
- Author:
Ruolin GUO
1
;
Yongqing SUN
;
Cuiying CAO
;
Yuan WANG
;
Yibin LIU
;
Yunfeng LI
;
Lijuan ZHANG
Author Information
1. 河北医科大学第二医院妇产科，石家庄 050000
- Publication Type:Journal Article
- Keywords:
Mayer-Rokitansky-Küster-Hauser syndrome;
Primordial uterus;
Endometrium;
Adenomyosis
- From:
Clinical Medicine of China
2025;41(6):471-475
- CountryChina
- Language:Chinese
-
Abstract:
Mayer-Rokitansky-Küster-Hauser (MRKH) syndrome is characterized by congenital vaginal hypoplasia and primordial uterus caused by Müllerian anomalies. Case reports concerning adenomyosis associated with MRKH syndrome are limited, and the formation and intervention of adenomyosis without endometrium are unclear. Here, we present the case of a patient with MRKH syndrome complicated with adenomyosis without endometrium, a hypoechoic solid mass next to the right ovary. According to the intraoperative observation and histopathological examination findings, the mass were diagnosed as adenomyosis of the primordial uterus. Moreover, our report provides insights about its mechanism of occurrence and interventions in MRKH syndrome combined with adenomyosis without endometrium.
