Progress in the treatment of primary ciliary dyskinesia in children
10.3760/cma.j.cn101070-20241128-00792
- VernacularTitle:儿童原发性纤毛运动障碍治疗研究进展
- Author:
Mengyue LI
1
;
Baoping XU
1
Author Information
1. 国家儿童医学中心，国家呼吸系统疾病临床医学研究中心，首都医科大学附属北京儿童医院呼吸中心临床部一病区；中国医学科学院儿童危重感染诊治创新单元；儿科重大疾病研究教育部重点实验室，北京 100045
- Publication Type:Journal Article
- Keywords:
Child;
Primary ciliary dyskinesia;
Treatment;
Prognosis
- From:
Chinese Journal of Applied Clinical Pediatrics
2025;40(11):873-876
- CountryChina
- Language:Chinese
-
Abstract:
Primary ciliary dyskinesia (PCD) is a rare hereditary disease caused by ciliary ultrastructure defects and functional disorders, with highly heterogeneous clinical manifestations.There is no specific treatment that can correct the ciliary dysfunction of PCD patients.Its treatment is usually based on the experience of similar diseases (such as cystic fibrosis), and also includes chest physical therapy, mucolytic agents and antibacterial drugs.The treatment method is closely related to the prognosis of patients.Thus, in this article, the treatment and prognosis of PCD in children were reviewed to provide a basis for its clinical treatment.
