Pulmonary Vein Stenosis: A Review
10.1097/CD9.0000000000000084
- VernacularTitle:Pulmonary Vein Stenosis: A Review
- Author:
Mengfei JIA
1
;
Juan WANG
;
Kaiyu JIANG
;
Hongling SU
;
Yu LI
;
Zhaoxia GUO
;
Hai ZHU
;
Aqian WANG
;
Xin PAN
;
Yunshan CAO
Author Information
1. The First Clinical Medical College of Gansu University of Chinese Medicine (Gansu Provincial Hospital), Lanzhou, Gansu 730000, China
- Publication Type:Journal Article
- Keywords:
Hypertension, pulmonary;
Pulmonary veins;
Stenosis;
Etiology;
Intervention
- From:
Cardiology Discovery
2023;03(2):127-137
- CountryChina
- Language:English
-
Abstract:
Pulmonary vein stenosis (PVS) is an extremely rare and lethal disease caused by multiple etiologies. PVS has a bimodal distribution in the population, affecting children and adults. Congenital PVS is the usual PVS type in children, which sometimes develops after cardiothoracic surgery. Acquired PVS, in turn, is the most common PVS type in adults. A review of the relevant literature has shown that PVS after radiofrequency ablation of atrial fibrillation is the most common, as well as that caused by compression of proliferative fibrous tissues or tumor in the mediastinum (eg, PVS caused by fibrosing mediastinitis, lung tumors, metastases, etc). This article provides a comprehensive review of PVS in terms of embryology and anatomy, etiology and triggers, classification, clinical symptoms and signs, treatment, and prognosis, intending to promote the understanding and treatment of this disease.