Clinical and imaging features of alveolar soft part sarcoma
10.3969/j.issn.1002-1671.2025.09.023
- VernacularTitle:腺泡状软组织肉瘤的临床及影像学特征
- Author:
Feng PAN
1
;
Anqi LI
1
;
Fei YUAN
1
Author Information
1. 北京大学人民医院放射科,北京 100044
- Publication Type:Journal Article
- Keywords:
alveolar soft part sarcoma;
soft tissue sarcoma;
computed tomography;
magnetic resonance imaging
- From:
Journal of Practical Radiology
2025;41(9):1529-1532
- CountryChina
- Language:Chinese
-
Abstract:
Objective To investigate the clinical and imaging features of alveolar soft part sarcoma(ASPS).Methods A retro-spective analysis was conducted on the clinical and imaging data of 41 patients with pathologically confirmed ASPS.Results The primary clinical manifestation of 41 patients with ASPS was progressive tumour enlargement.The tumors were located in the but-tocks(14 cases),thighs(11 cases),lower legs(5 cases),forearms(3 cases),upper arms(2 cases),psoas major muscles(2 cases),and one case each in the paracervical region,shoulder,axilla,and plantar regions.Pulmonary metastasis were observed in 30 patients,and 7 patients had metastases to other sites,including 2 cases of intracranial metastasis,1 case of lymph node metastasis,and 4 cases of bone and soft tissue metastasis.Five patients experienced postoperative local recurrence or metastasis.MR was performed in 34 patients,and CT was performed in 32 patients.The tumors were oval or irregular in shape.On CT,the tumors appeared as soft tissue density shadow,with calcification in 8 cases and 68％(17/25)showed marked enhancement with peripheral vascular plexus.On MR,the tumors exhibited isointense T1 and long T2 signals,67％(23/34)showed flow-void vessels within the tumor and 94％(32/34)showed tortuous vascular plexus at the tumor margins.Conclusion ASPS predominantly occurs in the muscles of buttocks and thigh and is prone to lung metastasis.Enhanced CT and MR can reveal vessels within and at the margins of the tumor,which is diagnosti-cally significant for ASPS.
