Pulmonary lymphangioleiomyomatosis complicated with pulmonary hypertension:a case report
10.3969/j.issn.1004-8812.2025.09.007
- VernacularTitle:肺淋巴管平滑肌瘤病合并肺高血压1例
- Author:
Jie ZHANG
1
;
Xiang-ting LU
1
;
Hai-long DAI
1
Author Information
1. 昆明医科大学附属延安医院心血管内科 云南省心血管疾病重点实验室 云南省心脏疾病临床医学中心,云南 昆明 650051
- Publication Type:Journal Article
- Keywords:
Pulmonary lymphangioleiomyomatosis;
Pulmonary hypertension;
Vascular endothelial growth factor-D
- From:
Chinese Journal of Interventional Cardiology
2025;33(9):532-535
- CountryChina
- Language:Chinese
-
Abstract:
Pulmonary lymphangioleiomyomatosis(PLAM)is a rare low-grade,destructive,and metastatic tumor characterized by diffuse cystic lesions in the lungs,mainly occurring in women of childbearing age.The occurrence of pulmonary hypertension(PH)in lung diseases often indicates poor prognosis,and case reports of PLAM combined with PH are relatively rare.This case report presents a 45 year old female patient with recurrent dyspnea as the main symptom.After completing relevant examinations such as right heart catheterization,echocardiography,chest CT,lung function,and vascular endothelial growth factor-D(VEGF-D),the diagnosis of PLAM combined with PH.This case report has important clinical significance for early diagnosis and corresponding measures for patients with PLAM combined with PH.
