Complicated VHL-associated bilateral adrenal pheochromocytomas in a child: a case report and literature review
10.3760/cma.j.cn115807-20250213-00047
- VernacularTitle:VHL相关儿童复杂双侧肾上腺嗜铬细胞瘤1例并文献复习
- Author:
Xu WANG
1
;
Yi XIE
1
;
Yushi ZHANG
1
;
Zhenyu ZHANG
1
;
Lin MA
1
Author Information
1. 中国医学科学院北京协和医院泌尿外科，北京 100730
- Publication Type:Journal Article
- Keywords:
VHL syndrome;
Gene mutation;
Pheochromocytoma
- From:
Chinese Journal of Endocrine Surgery
2025;19(3):453-455
- CountryChina
- Language:Chinese
-
Abstract:
Von Hippel-Lindau syndrome is a type of neoplastic disease that can involve multiple organs and systems, and it can be manifested as pheochromocytoma in the adrenal gland. We recently admitted a patient with a complicated bilateral adrenal pheochromocytomas associated with VHL in a child. After multidisciplinary diagnosis and treatment, detailed perioperative treatment and monitoring, the patient recovered well after surgery. This article aims to increase the experience of diagnosis and treatment of VHL-pheochromocytoma in children by sharing this rare case.
