An Adult Case of Double Chambered Right Ventricle after Interruption of Regular Follow-up for Ventricular Septal Defect
- VernacularTitle:心室中隔欠損症定期経過観察中断後成人期に診断された右室二腔症の1例
- Author:
Takako MIYAZAKI
1
;
Takeshi SHINKAWA
2
Author Information
- Keywords: double chambered right ventricle; ventricular septal defect; adult congenital heart disease
- From:Japanese Journal of Cardiovascular Surgery 2025;54(5):207-211
- CountryJapan
- Language:Japanese
- Abstract: We report an adult case of double chambered right ventricle (DCRV), in which right ventricular outflow tract stenosis is thought to have progressed after interruption of follow-up of ventricular septal defect (VSD). A 35-year-old female was diagnosed with VSD immediately after birth and had been hospitalized twice for infective endocarditis in infancy and childhood. More than 10 years after the interruption of regular follow-up, she visited her family doctor with a chief complaint of shortness of breath on exertion and chest pain, and was referred to our hospital for evaluation of VSD. Echocardiography showed VSD and DCRV. VSD was as small as 5×4 mm, but the maximum flow velocity at the DCRV stenosis was 4.87 m/s, which was judged to be an indication for surgical treatment. The patient underwent right ventricular stenosis release through the right atrium. Postoperative right ventricular stenosis was resolved. Since adult cases of DCRV are rare, and there is a lack of awareness of the disease concept and the nonspecific symptoms, it is difficult to diagnose DCRV in adults; so it is therefore important to treat patients with this disease concept in mind. In addition, it might be necessary to maintain follow-up with patients even with small VSD.
