Right pulmonary artery anterior translocation for Berry syndrome: Four cases report
- VernacularTitle:右肺动脉前移重建治疗Berry综合征四例
- Author:
Xucong SHI
1
;
Jianbin WENG
2
;
Jin YU
3
;
Xiaohui MA
4
;
Zhuo SHI
1
;
Jiangen YU
1
;
Xiangming FAN
1
Author Information
1. Department of Cardiac Surgery, Children s Hospital, Zhejiang University School of Medicine, National Clinical Research Center for Child Health, Hangzhou, 310052, P. R. China
2. Department of Neurosurgery, Children s Hospital, Zhejiang University School of Medicine, National Clinical Research Center for Child Health, Hangzhou, 310052, P. R. China
3. Department of Ultrasound Diagnosis, Children s Hospital, Zhejiang University School of Medicine, National Clinical Research Center for Child Health, Hangzhou, 310052, P. R. China
4. Department of Radiology, Children s Hospital, Zhejiang University School of Medicine, National Clinical Research Center for Child Health, Hangzhou, 310052, P. R. China
- Publication Type:Journal Article
- Keywords:
Berry syndrome;
primary correction;
right pulmonary artery anterior translocation;
pulmonary artery stenosis;
case report
- From:
Chinese Journal of Clinical Thoracic and Cardiovascular Surgery
2025;32(11):1672-1676
- CountryChina
- Language:Chinese
-
Abstract:
All four patients were female, with an average age of 28.8 days and an average weight of 3.64 kg. Only case 4 was born prematurely at 34 W+5 and was treated conservatively until 71 days to complete operation. All the others completed primary corrective surgery in the neonatal period, and all survived after operation. Two different surgical techniques were used to repair the aortic-pulmonary window and the aortic origin of the right pulmonary artery, including 1 case using the aortic internal baffle technique and another 3 cases underwent replantation of the right pulmonary artery (1 case was reconstructed in situ, and the other 2 cases were reconstructed by moving the right pulmonary artery in the anterior of aorta). Case 2 who received aortic internal baffle technique underwent two reoperation because of right pulmonary artery stenosis. While, right pulmonary artery of cases 3 and 4 developed well after being reconstructed the right pulmonary artery anterior translocation. After the diagnosis of Berry syndrome through cardiac color ultrasound and CT angiography, a primary surgical radical treatment should be performed as soon as possible at an experienced pediatric cardiac center. Although the surgery is high-risk and complex, it is safe and effective.
