A case of adult temporal bone langerhans cell histiocytosis presenting as posterior canal dehiscence syndrome and literature review.

Author: Dongzhou DENG ¹ ; Ying HU ² ; Dan BING ¹
Author Information

1. Department of Otolaryngology Head and Neck Surgery，Tongji Hospital，Tongji Medical College，Huazhong University of Science and Technology，Wuhan，430030，China.
2. Department of Radiology，Tongji Hospital，Tongji Medical College，Huazhong University of Science and Technology.
Publication Type:English Abstract
Keywords: langerhans cell histiocytosis; posterior semicircular canal dehiscence syndrome; tinnitus; vertigo
MeSH: Humans; Histiocytosis, Langerhans-Cell/complications*; Semicircular Canal Dehiscence/etiology*; Temporal Bone/pathology*
From: Journal of Clinical Otorhinolaryngology Head and Neck Surgery 2025;39(3):255-259
CountryChina
Language:Chinese
Abstract: This report describes a case of adult temporal bone Langerhans cell histiocytosis（LCH） that presented as posterior canal dehiscence syndrome（PCDS）. The patient initially presented with vertigo, tinnitus, and hearing loss. Computed tomography（CT） revealed erosive changes in the mastoid and posterior semicircular canal. After the operation, the patient's hearing and vestibular symptoms disappeared and postoperative recovery was favorable. Adult LCH is relatively rare, and this case serves as an example to discuss the clinical features and treatment options of this disease, followed by a literature review.