Pulmonary artery reconstruction to repair infant isolated unilateral absence of pulmonary artery: A retrospective cohort study in a single center
- VernacularTitle:肺动脉重建矫治婴幼儿孤立性单侧肺动脉缺如的单中心回顾性队列研究
- Author:
Xinjian YAN
1
;
Jimei CHEN
1
;
Jianzheng CEN
1
;
Shusheng WEN
1
;
Gang XU
1
;
Hujun CUI
1
;
Xiaobing LIU
1
;
Jian ZHUANG
1
Author Information
1. Department of Pediatric Cardiac Surgery, Guangdong Provincial People's Hospital, Guangdong Provincial Academy of Medical Sciences, Guangdong Institute of Cardiovascular Disease, Guangdong South China Key Laboratory of Structural Cardiology, Guangzhou, 510080, P. R. China
- Publication Type:Journal Article
- Keywords:
Pulmonary artery reconstruction;
unilateral absence of pulmonary artery;
congenital heart diseases
- From:
Chinese Journal of Clinical Thoracic and Cardiovascular Surgery
2024;31(04):600-605
- CountryChina
- Language:Chinese
-
Abstract:
Objective To confirm the changes of pulmonary artery pressure, neo pulmonary artery stenosis and reoperation in children with unilateral absence of pulmonary artery (UAPA) undergoing pulmonary artery reconstruction. Methods The clinical data of the infants with UAPA undergoing pulmonary artery reconstruction in our hospital from February 19, 2019 to April 15, 2021 were analyzed. Changes in pulmonary artery pressure, neo pulmonary artery stenosis and reoperation were followed up. Results Finally 5 patients were collected, including 4 males and 1 female. The operation age ranged from 13 days to 2.7 years. Cardiac contrast-enhanced CT scans were performed in all children, and 2 patients underwent pulmonary vein wedge angiography to confirm the diagnosis and preoperative evaluation. Preoperative transthoracic echocardiography and intraoperative direct pulmonary arterial pressure measurement indicated that all 5 children had pulmonary hypertension, with a mean pulmonary arterial pressure of 31.3±16.0 mm Hg. Pulmonary arterial pressure decreased immediately after pulmonary artery reconstruction to 16.8±4.2 mm Hg. The mean follow-up time was 18.9±4.7 months. All 5 patients survived during the follow-up period, and 1 patient had neo pulmonary artery stenosis or even occlusion and was re-operated. Conclusion Pulmonary artery reconstruction can effectively alleviate the pulmonary hypertension in children with UAPA. The patency of the neo pulmonary artery should be closely followed up after surgery, and re-pulmonary angioplasty should be performed if necessary.
