New onset refractory status epilepticus/febrile infection-related epilepsy syndrome: the new challenge in the diagnosis and treatment of status epilepticus
10.3760/cma.j.cn113694-20231030-00280
- VernacularTitle:新发难治性癫痫持续状态/热性感染相关性癫痫综合征：癫痫持续状态诊疗的新挑战
- Author:
Xuan WANG
1
;
Wen JIANG
Author Information
1. 空军军医大学西京医院神经内科，西安 710032
- Keywords:
New onset refractory status epilepticus;
Febrile infection-related epilepsy syndrome;
Drug resistant epilepsy;
Immunological treatment
- From:
Chinese Journal of Neurology
2024;57(4):309-314
- CountryChina
- Language:Chinese
-
Abstract:
New onset refractory status epilepticus (NORSE) and its subcategory, febrile infection-related epilepsy syndrome (FIRES) are rare and devastating conditions, initial symptoms of which are often refractory status epilepticus. NORSE/FIRES is characterized by high mortality and disability, but unfortunately, due to the unclear pathogenesis, the diagnosis and treatment of NORSE/FIRES are very challenging. This editorial aims to summarize the key points and recent developments in the etiology, pathophysiology, diagnosis and management of these challenging conditions.
