Dermatofibrosarcoma Protuberans of Parotid Region: A Case Report
10.21315/aos2023.1801.CR04
- Author:
Gabriel Xia Peng Quah
1
;
Siti Hajar Sanudin
2
;
Kar Yee Chiew
3
;
rfan Mohamad
4
Author Information
1. Department of Otorhinolaryngology, Hospital Queen Elizabeth, 88200 Kota Kinabalu, Sabah, Malaysia&Department of Otorhinolaryngology-Head and Neck Surgery, School of Medical Sciences, Universiti Sains Malaysia, 16150 Kota Bharu, Kelantan, Malaysia
2. Department of Otorhinolaryngology, Hospital Queen Elizabeth, 88200 Kota Kinabalu, Sabah, Malaysia&
3. Department of Pathology, Hospital Queen Elizabeth, 88200 Kota Kinabalu, Sabah, Malaysia
4. Department of Otorhinolaryngology-Head and Neck Surgery, School of Medical Sciences, Universiti Sains Malaysia, 16150 Kota Bharu, Kelantan, Malaysia
- Publication Type:Case Reports
- Keywords:
Dermatofibrosarcoma protuberans, fibrosarcomatous, head and neck, metastasis, parotid
- From:
Archives of Orofacial Sciences
2023;18(no.1):63-70
- CountryMalaysia
- Language:English
-
Abstract:
Dermatofibrosarcoma protuberans (DFSP) is a locally aggressive fibroblastic neoplasm that commonly
occurs in the trunk and extremities but rarely in the head and neck region. We report an atypical
presentation of DFSP with fibrosarcomatous transformation of the parotid region. A 34-year-old gentleman presented with a huge left parotid swelling that progressively increased in size over the past
seven years. He claimed that a biopsy of the swelling was done five years prior in another hospital and
he was told it was benign. He defaulted to follow-up as the lesion was painless initially but it started to
be painful and bleed intermittently one month before the presentation. Total parotidectomy was done
with the removal of adjacent enlarged lymph nodes but histopathological evaluation of the samples
showed fibrosarcomatous DFSP with positive margins. Unfortunately, the patient defaulted to follow-up again post-op and presented again after one year with extensive systemic metastasis. The dilemmas
in managing this case and suggestions for countermeasures together with references according to the
relevant literature are discussed.
- Full text:20.2023my00141.pdf
