1.Epidemiology, spectrum of clinical manifestations and diagnostic issue of acquired haemophilia: A case series
The Malaysian Journal of Pathology 2019;41(2):185-189
Introduction: Acquired haemophilia A (AHA) is a rare acquired bleeding disorder caused by polyclonal immunoglobulin G autoantibodies against clotting factor VIII (FVIII). The incidence was reported to be rare occurring in 0.2- 4 cases/million/year. Patients may present with different clinical manifestations to various specialties. Early recognition of the disease contributes to favourable clinical outcome. Case Series: Here, we reported five cases of this disorder with different clinical presentations from two tertiary hospitals in Kelantan state, Malaysia within a two year-period. Most of them were elderly, except for one who presented at the age of 36 years old. No direct or secondary cause was identified except for one patient who had developed from pregnancy-related at 3 weeks postpartum. These patients presented with spontaneous bleeding typically into skin, muscles, and mucous membranes but also at rare site in the epidural space. All patients denied previous history of bleeding or family history of bleeding disorder. FVIII activities were recorded between <1% to 19%, while the inhibitor titre levels were between 3.9 BU to 340 BU. The treatment approaches especially at presentation were complicated by unfamiliarity of managing this rare condition but all these patients received appropriate medical attention. Discussion: Prompt diagnosis and management in the right hand are critical. Awareness of this disorder by medical personnel at all levels in the community and in various specialties is important.
haemophilia
2.A Clinical Study and Comprehensive Total Care in Hemophilia.
Shin Heh KANG ; Chang Hyun YANG ; Kir Young KIM
Journal of the Korean Pediatric Society 1988;31(2):202-211
No abstract available.
Hemophilia A*
3.Clinical Studies on 100 Cases of Hemophilia.
Journal of the Korean Pediatric Society 1984;27(9):883-895
No abstract available.
Hemophilia A*
4.Management of hemophilia in Korea: the past, present, and future.
Blood Research 2014;49(3):144-145
No abstract available.
Hemophilia A*
;
Korea
5.Sickle cell-beta thalassemia with concomitant hemophilia A: a rare presentation.
Pratibha DHIMAN ; Rahul CHAUDHARY ; Krishna SUDHA
Blood Research 2015;50(4):264-267
No abstract available.
Hemophilia A*
;
Thalassemia*
6.Clinical characteristics in hemophilia patients.
Kun Soo LEE ; Eun Sook KIM ; Jang Soo SEO
Journal of the Korean Pediatric Society 1992;35(11):1501-1508
No abstract available.
Hemophilia A*
;
Humans
7.Attempts to treat patients with hemophilia, the "royal disease".
Blood Research 2013;48(4):235-236
No abstract available.
Hemophilia A*
;
Humans
8.Price of PRICE (Protection, Rest, Ice, Compression, and Elevation) redefined: a case of entrapment neuropathy in an individual with hemophilia.
Pritish Chandra PATRA ; Prakas Kumar MANDAL ; Debasis GANTAIT ; Amrita BHOWMIK ; Prantar CHAKRABARTI
Blood Research 2018;53(4):333-334
No abstract available.
Hemophilia A*
;
Ice*
9.The first case report of a patient with coexisting hemophilia B and Down syndrome.
Pulkit RASTOGI ; Narender KUMAR ; Jasmina AHLUWALIA ; Reena DAS ; Inusha PANIGRAHI
Blood Research 2017;52(1):75-76
No abstract available.
Down Syndrome*
;
Hemophilia A*
;
Hemophilia B*
;
Humans
10.Urgent craniectomy for subdural hematoma in the 8-month-old infant with unrecognized hemophilia B.
Jong Bun KIM ; Hyun Ju JUNG ; Kyong Shil IM ; Sang Woo HAN ; Sang Hun LEE
Korean Journal of Anesthesiology 2013;64(1):82-83
No abstract available.
Hematoma, Subdural
;
Hemophilia A
;
Hemophilia B
;
Humans
;
Infant
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