OBJECTIVE: To investigate imaging and audiology features of temporal bone and analyze the classification and prevalence of inner ear abnormalities in children with sensorineural hearing loss. METHOD: Children who were diagnosed with sensorineural hearing loss were examined by high resolution CT and the inner ear fluid of MRI. And each chart was retrospectively reviewed to determine the imaging and audiology features. RESULT: There were 125 patients(232 ears) found with inner ear malformation in 590 children with SNHL. About 21.71% of the inner ear malformation occurred in severe and profound hearing loss ears, and 12.85% occurred in r moderate hearing loss ears. The inner ear malformation rate in normal hearing ears were 13.59%. CONCLUSION CT and MRI examinations of temporal bone are important diagnostic tools to indentify inner ear malformations. Inner ear malformations are almost bilateral and hearing loss are profoud. Cochleo-vestibular malformations and large vestibular aqueduct are the 2 most frequent deformities. Among the children with SNHL, deformity rate in the severe and profound hearing loss ears is higher than that in moderate hearing loss ear. Inner ear malformations can exist in people with normal hearing.
Audiology ; Child ; Ear, Inner ; abnormalities ; Hearing Loss, Sensorineural ; congenital ; pathology ; Humans ; Magnetic Resonance Imaging ; Prevalence ; Retrospective Studies ; Temporal Bone ; Tomography, X-Ray Computed ; Vestibular Aqueduct ; abnormalities

A case report of multiple neuropathic arthropathy in a patient with syphilis was reported. A 54-year-old man was admitted to the hospital 10 years ago due to edema and pain with limited motion for 3 d after a sprain in his right foot. Imaging examination then showed bone and joint destruction of the talus and scaphoid of the right foot. The talonavicular and calcaneocuboid joint arthrodesis was performed. Ten years later, he was admitted again due to pain in his left hip for 2 months after a fall. Present imaging examination showed disappearance of the femoral head and dislocation of the hip joint. Syphilitic neuroarthropathy was diagnosed and total hip arthroplasty was performed. After operation, the right foot and left hip yielded good results without obvious pain and joint dislocation. Literature review showed that the causes of neuropathic arthropathy were very wide, but multiple neuropathic arthropathy in patients with syphilis was rarely reported. The treatment of neuropathic arthropathy should be considered based on comprehensive factors such as the location of the affected joint, the degree of damage and the impact on function. The aim of treatment is to obtain painless, stable and functional joints. With sensory loss of the patients, enhancing restriction of the joint during surgery is of importance to effectively prevent postoperative dislocation and obtain good function.