Objective To evaluate the diagnostic value of CT manifestations of the lung in localized Wegener′s granulomatosis(LWG). Methods CT findings of the lung in 11 patients with LWG verified by pathology were retrospectively analyzed. Results All the cases presented with multiple nodules of soft dense varying from 0.5 cm to 3.0 cm in diameter which distributed in the lung. Cavities were commonly seen in the larger nodules. Seven cases showed the wedge-shaped lesions with their bases situated externally on the pleural surface and with their convex apices directed at the hilum. The massive shadow with blurred margins was found in 4 cases. The nodules and wedge-shaped lesions demonstrated peripheral enhancement. Some of them presented with “vascular sign”. Conclusion The CT features of LWG were multiple nodules and cavities within nodules coexisting with wedge-shaped lesions, peripheral enhancement of nodules, and “vascular sign”. The law of change and the features of enhancement were relatively characteristic to the diagnosis of LWG.