No abstract available.
Child* ; Humans ; Nephrotic Syndrome*

No abstract available.
Thyroid Gland* ; Thyroid Nodule*

No abstract available.
Anemia ; Gaucher Disease* ; Humans ; Siblings* ; Thrombocytopenia

No abstract available.
Vitelline Duct*

No abstract available.
Thyrotropin*

Biliary atresia is a surgical disease of infancy with a very poor prognosis usually attributed to the rarity of surgically correctable case. This paper presents a case of incorrectable type of biliary atresia 50 days old Direan female infant who were subjected to the Modified Kasai Operation She had shown good bile excretion after surgery but developed recurrent fever, severe hypocalcemia and roentgenographically prover rickets during the follow up periods. She died 7 months after the operation.
Bile ; Biliary Atresia* ; Female ; Fever ; Follow-Up Studies ; Humans ; Hypocalcemia ; Infant ; Prognosis ; Rickets

OBJECTIVE: This study was proposed to evaluate the electrophysiologic changes in central motor conduction and in silent period (SP) after paraspinal transcutaneous electrical stimulation near caudal area of the spinal cord. METHOD: Conditioning stimulation was applied to T12 paraspinal area for 20 minutes using interferential current therapy (80~100 Hz) in 11 healthy subjects. The amplitude and latency of central motor conduction and duration of SP were measured in motor evoked potential (MEPs) by using magnetic stimulator, before and after the conditioning stimulation. These variables were recorded in both tibialis anterior muscle, innervated from stimulated spinal area, and both abductor pollicis brevis, innervated from cervical cord not directly stimulated by electrical stimulation. RESULTS: After conditioning stimulation, the amplitudes of central motor conduction decreased (p<0.01), and the latencies did not change in both cervical and lumbar muscles in transcranial and spinal MEP studies, and the duration of SP was decreased in same manner (p<0.01). CONCLUSION: These results mean that the excitability of anterior horn cells decreases and the supraspinal inhibitory mechanism of the central motor conduction is suppressed by a certain conditioned electrical cutaneous stimulation in entire spinal cord.
Anterior Horn Cells* ; Electric Stimulation* ; Evoked Potentials, Motor ; Muscles ; Spinal Cord ; Transcutaneous Electric Nerve Stimulation

CD4+/CD56+ hematodermic neoplasm is a rare and aggressive lesion that affects many organs, and skin involvement is highly characteristic. It is also termed blastic natural killer cell lymphoma in the World Health Organization classification. Several origins of tumor cells have been proposed, but recent studies have shown a relationship with plasmacytoid dendritic cells. A 2-year-old boy presented with multiple bruise-like violaceous subcutaneous nodules and plaques on the trunk, upper and lower extremities. Histological examination showed small-to-medium-sized blastoid cellular infiltration in the dermis and subcutaneous tissue. Tumor cells were positive for CD4, CD56 and TdT, and negative for CD8, CD20 and MPO. It primarily affects elderly patients, but, in this case, occurred in an infant. Due to its rarity, we present a case of CD4+/CD56+ hematodermic neoplasm affecting a pediatric patient.
Aged ; Dendritic Cells ; Dermis ; Humans ; Infant ; Killer Cells, Natural ; Lower Extremity ; Lymphoma ; Preschool Child ; Skin ; Subcutaneous Tissue ; World Health Organization

BACKGROUND: Allergic contact dermatitis (ACD) was once regarded as a disorder of the adult population, while ACD in children was considered rare. However, ACD in children may be more common than previously realized and more recently, it has been estimated that more than 20% of the pediatric population is affected by ACD. However, in Korea results of patch testing in the pediatric population has not yet been reported. OBJECTIVE: The purpose of this study was to analyze allergens responsible for ACD in Korean children and investigate the influence of sex, involved site, and atopic dermatitis on contact allergen sensitization. We also wanted to compare the results between the pediatric and the adult group. METHODS: A retrospective analysis of all patch test results from our data base between 2009 and 2011 was performed. A total of 234 patients were patch tested. The pediatric population was defined as patients 18 years and younger, and total 30 pediatric patients were included. RESULTS: A total of 30 patch tested cases (male 12, female 18) were analyzed. Overall, 66.7% of pediatric patients had at least one positive reaction and common allergens were nickel sulfate (33.3%), thimerosal (13.0%), and black rubber mix (10.0%) in order of frequency. There were no significant differences between contact allergen sensitivity and sex or involved sites. However, in the atopic group, the positive reactions to wool alcohols were significantly higher than in the non-atopic group (p=0.0076). In adults, common allergens were nickel sulfate (34.8%), p-tert butylphenol formaldehyde resin (11.8%), cobalt chloride (11.3%) and thimerosal (11.3%) in order of frequency. This was not significantly different to the pediatric group. CONCLUSION: ACD in children is not uncommon and patch testing in suspected children revealed 66.7% of positive reaction.
2-Naphthylamine ; Adult ; Alcohols ; Allergens ; Child ; Cobalt ; Dermatitis, Allergic Contact ; Dermatitis, Atopic ; Female ; Formaldehyde ; Humans ; Korea ; Nickel ; Patch Tests ; Pediatrics ; Phenylenediamines ; Retrospective Studies ; Rubber ; Thimerosal ; Wool

Superficial epithelioma with sebaceous differentiation (SESD) is a rare benign neoplasm that shows unique histologic features despite of the non-specific clinical findings. It is histopathologically characterized by a superficial multilobular plate-like proliferation of basaloid cells with clusters of sebocytes, and the plate-like proliferation has numerous broad attachments to the overlying epidermis. We report here on a case of multiple SESDs that presented on the trunk and extremities of 59-year-old woman.
Carcinoma ; Epidermis ; Extremities ; Female ; Humans ; Middle Aged