Histiocytosis X is characterized by aggregates of Langerhans cells with other inflammatory cells. These Langerhans cells are antigen-presenting cells to T lymphocytes and identified by characteristic morphology, ultrastructural demonstration of Birbeck granules and immunologic reactivity with OKT-6 and HLA-DR antibodies. In this report, the tumor arising in a 2-years-old baby was examined byimmunostaining with several macrophage/dendritic cell markers. The main tumor cells showed cytoplasmic and nuclear staining with S-100 protein and ring-like surface and paranuclear staining with PNA. However, they were negative for follicular dendritic cell marker CD21, macrophage markers lysozyme, Mac 387, alpha-1 antitrypsin and CD68, and interdigitating reticulum cell marker ID4 and ID5. These observations demonstrate the usefulness of S-100 protein and PNA for the identification of Langerhans cells in paraffin-embedded tissue.

Congenital hepatic fibrosis is an inherited, congenital disorder of the liver, and is occasionally associated with cystic disease of the liver and kidney. We present a case of congenital hepatic fibrosis with Caroli's disease. A 21-year-old woman had suffered from an episodic fever with headaches for 3 years. In laboratory examination, the liver function test was within the normal limits. Esophageal varix was noted by an endoscopic examination. Hepatosplenomegaly and multiple dilated bile ducts were seen by abdominal CT scanning. An orthotopic whole liver transplantation was done. The liver was fibrotic and enlarged. Multiple cystically dilated intrahepatic ducts were noted. Microscopically, diffuse portal fibrosis and widening with proliferation of bile ductules were seen. Intrahepatic bile ducts were markedly dilated and tortuous. The liver cell cords were well preserved.
Bile ; Bile Ducts ; Bile Ducts, Intrahepatic ; Caroli Disease* ; Congenital, Hereditary, and Neonatal Diseases and Abnormalities ; Esophageal and Gastric Varices ; Female ; Fever ; Fibrosis* ; Headache ; Humans ; Kidney ; Liver ; Liver Function Tests ; Liver Transplantation ; Tomography, X-Ray Computed ; Young Adult

No abstract available.
Knee Joint* ; Knee* ; Torque*

No abstract available.
Psoriasis

Purpose: The purpose of this study was to identify factors influencing nurses’ performance of care in COVID-19 wards. Methods: The participants were 132 nurses who worked in COVID-19 wards at three hospitals, and were recruited from April 1 to May 31, 2021. Data were analyzed using descriptive statistics, t-test, ANOVA, and multiple regression analysis with SPSS/WIN 24.0 program. Results: Nursing performance was significantly and positively correlated with ethical sensitivity (r = .75, p < .001), nursing professionalism (r = .67, p < .001), and social support (r = .67, p < .001). Nursing professionalism was positively correlated with ethical sensitivity (r = .64, p < .001) and social support (r = .55, p < .001). Multiple regression analysis for nursing performance revealed that the most significant factor was ethical sensitivity (β = .47, p < .001). Ethical sensitivity, nursing professionalism, and social support explained 66.0% of total variance in nursing performance. Conclusion Ethical sensitiviy, nursing professionalism, and social support significantly influence nurses’ performace of care in COVID-19 wards. It suggests that intervention programs should be directed at improving nurses’ ethical sensitivity, bolstering social support, and enhancing nursing professionalism.

No abstract available.

PURPOSE: To obtain guideline of diagnosis and treatment when hyperdeviation associated with intermittent exotropia shows symptoms similar to superior oblique palsy (SOP). METHODS: We reviewed the charts retrospectively in 27 patients showing simulated SOP in intermittent exotropia, in which hyperdeviation in primary gaze and 10PD or more by Bielschowsky head tilt test were present. Overaction of Inferior oblique, (IOOA) dysfunction of superior oblique, and forveal extorsion more than +2 were excluded including reoperation and head tilt history. All patients were undergone horizontal muscle surgery only. The postoperative changes of deviation were analyzed at postoperative one day, one month, six month, and one year. RESULTS: Average amount of distant horizontal deviation in primary gaze was 32.3+/-9.58PD. Hyperdeviation was 3.8+/-2.52PD. Degree of IOOA averaged +1.18 in hypertropic eye, and +1.06 in hypotropic eye. Only 10 patients (37%) had foveal extorsion less than +2 in degree. Average vertical deviation of hypertropic eye side was 12.7+/-2.93PD on head tilt test. After horizontal surgery only, the amount of hyperdeviation decreased to 1.3PD at 1st day. On head tilt test, hyperdeviation was almost eliminated showing 0.6PD on the hypertropic side and 0.1PD on the contralateral eye at one month. All patients were aligned up to the follow-up of one year. CONCLUSIONS: To differentiate simulated SOP from intermittent exotropia with hyperdeviation, none of head tilt history, mild foveal extorsion, mild oblique dysfunction less than +3, double Maddox rod test, and forced duction test are important guidelines. Horizontal muscle surgery is only needed to remove exodeviation and hyperdeviation.
Diagnosis ; Exotropia* ; Follow-Up Studies ; Head ; Humans ; Paralysis* ; Reoperation ; Retrospective Studies

Background: Post-dural puncture headache (PDPH) is one of the well-known complication of spinal anesthesia. Epidural blood patch is the treatment of choice for PDPH but is rarely used for the prevention of PDPH after spinal anesthesia. The purpose of this study is to observe the effectiveness of epidural blood patch for prevention of PDPH and to evaluate the complications after epidural blood injection. Methods: Three hundred patients (ASA I or II) receiving spinal anesthesia were studied. They were randomly devided into two groups. Patients in Group I, the control group, were maintained in a supine position for 24 hour after spinal anesthesia. Patients in Group II, the study group, received 3 ml of autologous blood in the epidural space after spinal anesthesia. PDPH was evaluated for 5 days. The incidence, location, onset, and duration of headache in the patients presenting with PDPH were measured for 5 days, and the complications following epidural blood patch in Group II were observed for 2 weeks. Results: The incidence of PDPH in group I was 11%, but 0% in group II. There were no specific complications following epidural blood patch in Group II. Conclusions: This study suggest that the 3 ml epidural autologous blood patch is an useful method for the prevention of PDPH in patients with spinal anesthesia.
Anesthesia, Spinal* ; Blood Patch, Epidural ; Epidural Space ; Headache ; Humans ; Incidence ; Post-Dural Puncture Headache ; Punctures* ; Supine Position

Congenital anophthalmos is fairly rare malformation in which the eyeball is apparently absent. We experienced a 10-day-old boy, who had a congenital anophthalmos of his left eye, a microphthalmos of the other eye and short palpebral fissure of both eyes(right: 12mm, left: 5mm). The absence of left eyeball within a small orbit was confirmed by C-T scanning. We report this interesting case with a brief review of literatures.
Anophthalmos* ; Humans ; Male ; Microphthalmos ; Orbit

It is important to detect binocular suppression of pediatric strabismic patients, especially in accommodative esotropes and intermittent exotropes. However, it may take a long time and false results may be obtained in young children. In order to examine binocular suppression, we selected 103 accommodative esotropes with binocular suppression. Vectograph test, Worth 4 dot test, and 4 prism base-out test were performed at distance, and Worth 4 dot test, TNO test, and Bagolini test at near. Titmus fly test and Randot stereotest were administerd to know the relationship between stereoacuity and suppression. In detecting binocular suppression, the true rate of vectogram was 95%, which was the highest result of all tests and 4 prism base-out test was the next with 88% of the true rate. The stereoacuity was increased in proportional to the absence of suppression. The vectographic porject test was the easiest and the most accurate test to identify normal fusion or binocular suppression at distance in young strabismic children. The accuracy will be increased in the combination with 4 prism base-out test. Therefore the vectograph also can be used in the screening of small amount of deviation, monocular amblyopia and low vision in kindergarten and elementary school.
Amblyopia ; Child ; Diptera ; Humans ; Mass Screening ; Telescopes* ; Vision, Low