Incontinentia pigmenti is an uncommon genodermatosis. It affects female infants predominantly, described first by Bardach in l925, with the diagnosis of systematized nevus and Bloch in 1926, and Sulzberger in 1928 rnore compIetely. Skin lesions are characterized by 3 stages such as vesicobullous, verucous and finally pigmentary lesions and leave brownish pigmentation on the extremities and trunk. Hesides skin lesions some ectodermaI and mesodermal organs are affected and show developmental abnormalities. We experienced a case of incontinentia pigmenti in a 45-day-old female infant and present it with the review of literature. She showed extensive vesicobullopustular eruption with linear and reticular pigmentation on the extremities and trunk. Clinical and histopathologic findings of these lesions are compatible with Bloch-Sulzberger type of incontinentia pigmenti.
Diagnosis ; Extremities ; Female ; Humans ; Incontinentia Pigmenti* ; Infant ; Mesoderm ; Nevus ; Pigmentation ; Skin

After dual plating with a locking compression plate for comminuted intraarticular fractures of the distal humerus, the incidence of ulnar nerve injury after surgery has been reported to be up to 38%. This can be reduced by an anterior transposition of the ulnar nerve but some surgeons believe that extensive handling of the nerve with transposition can increase the risk of an ulnar nerve dysfunction. This paper reports ulnar nerve injuries caused by the incomplete insertion of a screw head in dual plating without an anterior ulnar nerve transposition for AO/OTA type C2 distal humerus fractures. When an anatomical locking plate is applied to a distal humeral fracture, locking screws around the ulnar nerve should be inserted fully without protrusion of the screw because an incompletely inserted screw can cause irritation or injury to the ulnar nerve because the screw head in the locking system usually has a slightly sharp edge because screw head has threads. If the change in insertion angle and resulting protruded head of the screw are unavoidable for firm fixation of fracture, the anterior transposition of the ulnar nerve is recommended over a soft tissue shield.
Head* ; Humeral Fractures ; Humerus* ; Incidence ; Intra-Articular Fractures ; Surgeons ; Ulnar Nerve*

No abstract available.
Craniosynostoses*

Pseudohypoparathyroidism is a medical disorder characterized by a complex disorder of renal resistance to parathyroid hormone and the mechanism underlying the disease is still unclear. The authors described two cases of pseudohypoparathyroidism in sibling,who had metabolic anomalies(hypocalcemia and hyperphosphatemia, high circulatin immunoreactive PTH)and basal ganglia calcification. Bilateral basal ganglia calcifications, which was not visible on plain skull film, was detected by CT scan of brain MRI. We report these cases with a review of related literatures.
Basal Ganglia ; Brain ; Humans ; Hyperphosphatemia ; Magnetic Resonance Imaging ; Parathyroid Hormone ; Pseudohypoparathyroidism* ; Siblings* ; Skull ; Tomography, X-Ray Computed

A persistent left superior vena cava is the most common anomaly of the superior caval system. Usually the persistent left superior vena cava is connected with the right atrium via the coronary sinus, resulting in no physiologic derangement : however in 7 to 8 percents of the patietns with a persistent left superior vena cava, the anomalous vessel communicates with the left atrim. In the absence of obstruction to the flow from the left atrium to the left ventricle. this anatomic situation usually results in right to left shunting of varying degress. We recently experienced a case of persistent left superior vena cava in a 52-year-old female who complained of chest discomfort, epigastric pain and dyspnea(NYHA functional class II). Cine-angiography showed that the contrast passed from the left SVC through the dilated coronary sinus into right atrium. And right sided SVC was not seen. The patient was treated with conservative measures and discharged with improved condition.
Coronary Sinus ; Female ; Heart Atria ; Heart Ventricles ; Humans ; Middle Aged ; Thorax ; Tricuspid Valve Insufficiency* ; Vena Cava, Superior

PURPOSE: To assess CT findings of pulmonary sarcoidosis and correlate these with sACE level and PFT. MATERIALS AND METHODS: Between 1989 and 1995, 14 patients (4 men and 10 women, aged between 28 and 55 years) with histologically confirmed pulmonary sarcoidosis were consecutively selected. HRCT scans were performed in 12 patients and conventional CT scans in two. CT findings were reviewed by three radiologists, and were correlated with the index of disease activity based on sACE level and pulmonary function test. RESULTS: Pulmonary parenchymal abnormalities were seen in all patients ; small nodules of less than 3 mm in diameter were seen in eight. Other abnormalities were nodules of more than 3 mm in diameter (n=7), confluent nodules (n=5), ground glass opacity (n=5), patchy areas of consolidation with air bronchogram (n=5), and architectural distortion (n=3). The upper lung zone was more frequently involved than the middle or lower zone. In ten patients, the peripheral interstitum was predominantly involved, while only three patients showed predominant peribronchovascular involvement. Lymphadenopathy was noted in 13. There was no correlation between sACE level, the results of a pulmonary function test and the extent of parenchymal involvement. CONCLUSION: HRCT is valuable for the identification, characterization, and determination of the extent to which parenchymal lung is involved in sarcoidosis. The extent of this involvement does not correlate with sACE level and pulmonary function test results.
Female ; Glass ; Humans ; Lung ; Lymphatic Diseases ; Male ; Respiratory Function Tests ; Sarcoidosis ; Sarcoidosis, Pulmonary* ; Tomography, X-Ray Computed

PURPOSE: To determine the upper limit of peripheral nerve lengthening without loss of function, the recovery time of peripheral nerve palsy due to nerve lengthening and their histological changes. MATERIALS AND METHODS: Twelve adult New Zealand rabbits weighing about 2.5 kg were assigned to the following groups. Group 1 (n=6) was subjected to slow tissue expansion with 30% of nerve lengthening while group 2 (n=6) was rapid expansion with 40% lengthening of nerve. The expanders were refilled every 2 times during the 2nd and 4th weeks making a total four times of expansion. The rabbits were assessed in terms of affected leg paralysis, neural length gain, EMG with nerve conduction velocity and histological changes. RESULTS: In group 1 (n=6), paralysis on affected leg was found in one rabbit and was recovered spontaneously on the 4th weeks after expander removal. In Group 2 (n=6), paralysis was found in four rabbits, and three of them were recovered on 4, 5 and 9 weeks after removal of the expander. EMG study showed increase in distal latency of 2.50+/- 0.20 m/sec, and decrease in nerve conduction velocity of 62.49+/- 5.30 m/sec compared to normal side with 1.89+/- 0.14 m/sec and 75.39+/- 7.82 m/sec. The mean neural length gain was 6 mm (30% of 20 mm of initial pre-experimental nerve length) in group 1 and 8 mm (40% of 20 mm) in group 2. Light microscopic examination revealed the loss of segmental myelination, decrease of myelination, and vacuolation. Electron microscopic examination showed that the normal ring shaped contour of axon was changed to convoluted shape.
Adult ; Axons ; Humans ; Leg ; Myelin Sheath ; Nerve Expansion ; Neural Conduction ; Paralysis ; Peripheral Nerves ; Rabbits ; Sciatic Nerve* ; Tissue Expansion*

Recently, the Korean Neuropsychiatric Association (KCNP) has been expanded greatly in the number of members as well as the qualities in the area of practice and research. There are also 23 affiliated academic societies : Korean Academy of Psychotherapists, Korean Society for Analytical Psychology, the Korean Psychoanalytic Society, the Korean Association for Clinical Art, Korean Academy of Child & Adolescent Psychiatry, the Korean Association of Social Psychiatry, The Korean Society of Biological Therapies in Psychiatry, Korean College of Neuropsychopharmacology, the Korean Society of Biological Psychiatry, Society of Korean Women Psychiatrists, the Korean Society of Clinical Hypnosis, the Society for Human Sexuality, Korean Society of Sleep Research, the Korean Society for Psychopathology and Psychiatric Classification, Korean Academy of Psychiatry and the Law, Korean Psychosomatic Society, Korean Academy of Sleep Medicine, Korean Association for Geriatic Psychiatry, Korean Academy of Psychiatrists in Alcoholism & Addiction, Korean Academy of Adolescent Psychiatry, Korean Academy Schizophrenia, Korean Society for Depressive and Bipolar Disorders, and Korean Academy of Anxiety Disorders. To further encourage the progress of the KCNP affiliated academic societies, the KCNP planning committee has developed the proposed criteria for assessing the societies.
Adolescent ; Adolescent Psychiatry ; Alcoholism ; Anxiety Disorders ; Biological Psychiatry ; Biological Therapy ; Bipolar Disorder ; Child ; Classification ; Community Psychiatry ; Female ; Humans ; Hypnosis ; Jurisprudence ; Psychiatry ; Psychology ; Psychopathology ; Schizophrenia ; Sexuality

Plunging nasal tip is named on all situations with a long and drooping nose at rest. The severity increases with aging. Morphologically, the nose appears to invade the upper lip, which causes cosmetic problems. In more severe cases, the inspired air flow may be disturbed, leading to functional nasal obstruction. Plunging nasal tip is occasionally termed as smiling tip by some authors. We have classified the plunging nasal tip into 3 categories, based on the McCarthy's classification but with modification, which is more suitable for Asians. The study was undertaken with patients whose nasal tip looks like invade the upper lip, even at rest. In Type I(severe type) the nasal septum is long, invading the lip, and with intact attachment of the alar cartilage to the septal angle. Type II(moderate to mild type) is when the loose attachment of the alar cartilage to the septal angle makes the nasal tip appear drooping, but those less severe than type I. In Type III(pseudo type) the location of the nasal tip is relatively appropriate but, due to maxillary protrusion, the tip looks as if it covers the upper lip. The open rhinoplasty technique was applied regardless of the classified type. Dorsal augmentation, tip plasty, interdomal suture of alar cartilage or detatchment of depressor septi nasi muscle were selectively used when required in all patients. In type I, the removal of caudal septum, cephalic lateral crus resection, anchoring suture of the alar cartilage on the septal angle, and columella strut were concomitantly undertaken. The resection of the cephalic lateral crus, anchoring suture of the alar cartilage on the septal angle and columella strut were applied in type 2. Cephlic lateral crus resection and columella strut were done in type 3. We have made a follow up on 13 patients for up to 6.5 years, who had undergone surgery between March, 1993 to september, 2001. We could get excellent results with no definite re-drooping of nasal tip in all cases.
Aging ; Asian Continental Ancestry Group ; Cartilage ; Classification* ; Follow-Up Studies ; Humans ; Lip ; Nasal Obstruction ; Nasal Septum ; Nose ; Rhinoplasty* ; Smiling ; Sutures

Infected aneurysm of the aorta is a rare but life-threatening condition. The traditional strategy for treating infected aortic aneurysms is open surgical repair with antibiotic therapy. Endovascular repair of infected aortic aneurysms has been performed only sporadically. Case: A 70-year-old man with a history of diabetes who presented with intermittent fever for one month was referred to our institution. Before admission, antibiotic treatment had been already started and on admission, his general condition was not critical. A CT scan showed two saccular aneurysms of the infrarenal abdominal aorta and a retroperitoneal inflammation including hematoma. No microorganism was identified on blood culture. On follow-up CT scan 15 days later, a further increase in aneurysmal diameter was detected and endovascular repair was performed by using Gore Excluder stent graft. The patient was recovered and discharged on hospital day 29. One month after discharge, the patient was readmitted due to chilling and fever. Abdominal CT showed a retroperitoneal abscess around the previously repaired aortic aneurysm. Surgical drainage was performed without reconstruction with extra-anatomical bypass or in situ replacement. Culture from the abscess revealed the growth of Klebsiella pneumoniae. The patient was discharged on postoperative day 31 and continues to be observed.
Abscess* ; Aged ; Aneurysm ; Aneurysm, Infected ; Aorta ; Aorta, Abdominal ; Aortic Aneurysm ; Aortic Aneurysm, Abdominal* ; Blood Vessel Prosthesis ; Drainage ; Fever ; Follow-Up Studies ; Hematoma ; Humans ; Inflammation ; Klebsiella pneumoniae ; Tomography, X-Ray Computed