No abstract available.
Urticaria Pigmentosa* ; Urticaria*

No abstract available.
Humans ; Infant* ; Male* ; Urticaria Pigmentosa* ; Urticaria*

Urticaria pigmentosa is a form of urticaria characterized by abnormality of cutaneous mast cells. No prediction for either gender has been reported but it usually occurs in children. When it develops in an adult cutaneous manifestations often follows recalcitrant and persistent course. Though tendency of genetic inheritance with an autosomal dominant pattern has been suggested most of patients have no family history of mastocytosis. We report a case of adult-onset urticaria pigmentosa with references.
Adult ; Child ; Humans ; Mast Cells ; Mastocytosis ; Urticaria Pigmentosa* ; Urticaria* ; Wills

We report three cases of atypical skin eruptions in leukemias presenting as scrotal ulcers, herpes simplex and urticaria pigmentosa that are unique in their morphology and site of presentation. Therefore any skin lesion that develops in patients with leukemia should be examined by biopsy.
Biopsy ; Herpes Simplex ; Humans ; Leukemia* ; Skin* ; Ulcer ; Urticaria Pigmentosa

Seoul, Korea Cutaneous mastocytosis is primarily a disease of children and its onset in adults life is rare. When it develops in adult, lesions appear as urticaria pigmentosa in most cases, and rarely as telangiectasia macularis eruptiva perstans. We report herein a case of cutaneous mastocytosis which appeared for the first time around the age of 40 with mixed or intermediate form of urticaria pigmentosa and telangiectasia macularis eruptiva perstans clinically, and histologically.
Adult ; Child ; Humans ; Korea ; Mastocytosis, Cutaneous* ; Seoul ; Telangiectasis ; Urticaria Pigmentosa

Urticaria pigmentosa is a manifestation of mastocytosis characterized by persistent pigmented cutaneous lesions of various size that tend to urticate upon mechanical or chemical irritation, The disease is most common in ehildren and skin lesions after appear within 1 or 2 months of birth. Urticaria pigmentosa in children begins with disseminated eruption (buIlou type) or with a solitary tumor or nodule(solitary type). One case. of solitary type and one case of bullous type are reported in this paper. The one case is a solitary type of urticaria pigmentosa in 1 1/2 years old male who had dark brownish pigmented nodule(2.5 1cm) on right hack since 1 year ago. Tie other is a bullous type of urticaria pigmentousa in 6 months old male who had generalizcd. bulla, hemorragic bulla with crust & millium since 4 months ago. Dignosis was confirmed by histologic findings in which showed infiltration of mast cells in upper nr entire dermis arui rnetachromatic granules in mast cell on toluidine blue stain. Literature were reviewed briefly.
Child ; Dermis ; Humans ; Infant ; Male ; Mast Cells ; Mastocytosis ; Parturition ; Skin ; Tolonium Chloride ; Urticaria Pigmentosa* ; Urticaria*

Urticaria pigmentosa developed in twins at the age of 6 weeks. They have numerous round to oval shaped, discrete or confluent reddish brown colored macules over whole body surface and neither twin had vomiting, diarrhea, flushing or irritability. Their relatives are unaffected. Biopsy specimen of. back lesion showed. pooling of mast cells in the upper dermis, and electron microscopic examinattion revealed normal mast cells.
Biopsy ; Dermis ; Diarrhea ; Flushing ; Humans ; Mast Cells ; Twins* ; Urticaria Pigmentosa* ; Urticaria* ; Vomiting

Urticaria pigmentosa (UP) is the most common variant of cutaneous mastocytosis. Primarily a disease of childhood, in over one-half of the cases onset is before 2 years of age, and in 90%, the disease is confined to the skin. UP precedes the diagnosis of systemic mastocytosis and is more common in adults than in children. Therefore, systemic examination should be performed in patients with UP. We report a case of adult-onset UP with systemic involvement.
Adult ; Child ; Humans ; Mastocytosis, Cutaneous ; Mastocytosis, Systemic ; Skin ; Urticaria ; Urticaria Pigmentosa

Mastocytosis is a heterogenous group of disorders characterized by the proliferation and accumulation of mast cells in a variety of tissues, most often skin. Urticaria pigmentosa is the most common type of cutaneous mastocytosis in both adults and children. However, the clinical manifestation of adult-onset urticaria pigmentosa may have some differences such as smaller macules, more pruritic symptoms, and frequent association with systemic symptoms. We report a case of adult-onset urticaria pigmentosa in a 51-year-old woman which we compare to those cases reported in the literatures.
Adult ; Child ; Female ; Humans ; Mast Cells ; Mastocytosis ; Mastocytosis, Cutaneous ; Middle Aged ; Skin ; Urticaria Pigmentosa* ; Urticaria*

We observed 2 cases of urticaria pigmentosa with synchronous onset and concordant manifestation in a pair of identical male twins. At the age of 12 months both had developed multiple, round-to-oval, discrete brown-colored macules on the trunk and extremities. They had no systemic manifestations. Biopsy specimens in both cases showed the presence of a number of mast cells in the papillary and superficial dermis. We, herein, describe a pair of monozygotic twins with urticaria pigmentosa.
Biopsy ; Dermis ; Extremities ; Humans ; Male ; Mast Cells ; Twins, Monozygotic* ; Urticaria Pigmentosa* ; Urticaria*