1.Immunoglobulin G4-Related Sclerosing Disease Involving the Urethra: Case Report.
Jin Woo CHOI ; Sang Youn KIM ; Kyung Chul MOON ; Jeong Yeon CHO ; Seung Hyup KIM
Korean Journal of Radiology 2012;13(6):803-807
Immunoglobulin G4 (IgG4)-related sclerosing disease is a systemic disease characterized by extensive IgG4-positive plasma cells and T-lymphocyte infiltration in various organs. We described the imaging findings of an IgG4-related inflammatory pseudotumor in the urethra. The urethral mass showed isoattenuation on unenhanced CT images, delayed enhancement on enhanced CT images, iso- to slight hyper-intensity on T1 and T2 weighted magnetic resonance images, diffusion restriction on diffusion weighted images, and heterogeneously low echogeneity on ultrasonography.
Aged
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Autoimmune Diseases/diagnosis
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Female
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Granuloma, Plasma Cell/*diagnosis
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Humans
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Immunoglobulin G/*immunology
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Pancreatitis/diagnosis/immunology
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Sclerosis
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Urethral Diseases/*diagnosis/immunology