1.Malignant Peripheral Nerve Sheath Tumor in Neurofibromatosis Type I: Unusual Presentation of Intraabdominal or Intrathoracic Mass.
Jong Gwang KIM ; Woo Jin SUNG ; Dong Hwan KIM ; Young Hwan KIM ; Sang Kyun SOHN ; Kyu Bo LEE
The Korean Journal of Internal Medicine 2005;20(1):100-104
A malignant peripheral nerve sheath tumor (MPNST) is an extremely rare soft tissue tumor in the general population. On the other hand, there is a higher incidence of MPNST in patients with neurofibromatosis type I (von Recklinghausen's disease). The common sites are the extremities, trunk, head and neck. However, an intraabdominal or intrathoracic manifestation is uncommon. This paper reports two patients, a 31 year-old woman with multiple neurofibromatosis presenting as an intraabdominal malignant peripheral nerve sheath tumor, and a 33 year-old woman with an intrathoracic malignant peripheral nerve sheath tumor. The patients were treated with chemotherapy followed by radiotherapy. However, one patient died as a result of disease progression 21 months after the diagnosis and the other patient is currently being treated with radiotherapy.
Abdominal Neoplasms/*diagnosis
;
Adult
;
Female
;
Humans
;
Nerve Sheath Tumors/*diagnosis
;
Neurofibromatosis 1/*complications
;
Thoracic Neoplasms/*diagnosis
2.Carcinoma Originating from Aberrant Breast Tissue of the Right Upper Anterior Chest Wall : A Case Report.
Ji Young RHO ; Seon Kwan JUHNG ; Ki Jung YOON
Journal of Korean Medical Science 2001;16(4):519-521
Aberrant breast tissue is usually found in proximity to the normal breast, that is, in the axillary, sternal or clavicular regions. Carcinoma occurs more frequently in the aberrant tissue of the axilla than the extra-axillary site though the overall incidence of tumors of aberrant breast tissue is low. To our knowledge, studies regarding the carcinoma of aberrant breast tissue of the extra-axillary site have been reported rarely. Here we report a recent case of carcinoma originating from the extra-axillary aberrant breast tissue, presenting as a subcutaneous nodule on the right upper anterior chest wall. It is suggested that subcutaneous nodules of uncertain origin around the periphery of the breast should be suspected for breast carcinoma as a differential diagnosis and treated properly.
Breast Neoplasms/*diagnosis
;
Choristoma/*diagnosis
;
Diagnosis, Differential
;
Female
;
Human
;
Middle Age
;
Thoracic Neoplasms/*diagnosis
;
Tomography, X-Ray Computed
3.An aortic arch anomaly protruding into the esophagus misdiagnosed as leiomyoma of the esophagus.
Xionghuai HUA ; Wei ZHANG ; Yin LI
Chinese Medical Journal 2014;127(15):2879-2879
Aorta, Thoracic
;
abnormalities
;
Esophageal Neoplasms
;
diagnosis
;
Humans
;
Leiomyoma
;
diagnosis
;
Male
;
Middle Aged
4.The diagnosis and management for child cervical and thoracic angio lymphoma (3 cases report).
Jun WANG ; Weihong XIN ; Qianqian CHEN ; Jian YUE ; Yingnan KAN ; Jiajing ZHU ; Ping YAO
Journal of Clinical Otorhinolaryngology Head and Neck Surgery 2010;24(7):306-310
OBJECTIVE:
To discuss the diagnosis and treatment of child cervical and thoracic angio lymphoma.
METHOD:
Three cases of huge cervicothoracic angio lymphoma were performed by cervicothoracic approach and median split of sternum under general anesthesia.
RESULT:
The pathological diagnosis of three cases were angio lymphoma, and there was no recurrence and complication during the follow-up.
CONCLUSION
The tumor could be fully exposed by cervicothoracic approach operation, which was the basic guarantee for completely revealed tumor, and no recurrence was found. Other treatment should not be recommend for huge cervicothoracic angio lymphoma.
Child
;
Child, Preschool
;
Female
;
Humans
;
Lymphangioma
;
diagnosis
;
surgery
;
Male
;
Neck
;
Thoracic Neoplasms
;
diagnosis
;
surgery
5.Epithelioid Myofibroblastoma of Mammary-type in Chest Wall: A Case Report.
Hyun Jung KIM ; Hunkyung LEE ; Ok Jun LEE ; Kyung Ja CHO ; Jae Y RO
Korean Journal of Pathology 2005;39(2):130-133
Mammary-type myofibroblastoma of the soft tissue is a benign mesenchymal tumor, and it is a recently established clinical entity. We report a case of myofibroblastoma of the chest wall with a prominent epithelioid feature, that occurred in a 12-year old female. Although the lesion occurred in the breast area, there was no breast parenchyma in or around the mass, which favored soft tissue of the chest wall origin. The tumor was immunohistochemically identical to the mammary-type myofibroblastoma with diffuse and strong positivity against CD34 and desmin. The myoepithelial differentiation of the tumor was further supported by the electron microscopic analysis. This case indicates that mammary-type myofibroblastoma can occur in a young girl. The mammary-type myofibroblastoma should be considered a differential diagnosis, among epithelioid soft tissue neoplasms in the chest wall when the proper immunohistochemical work-up is done.
Breast
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Child
;
Desmin
;
Diagnosis, Differential
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Female
;
Humans
;
Neoplasms, Muscle Tissue*
;
Soft Tissue Neoplasms
;
Thoracic Wall*
;
Thorax*
6.Preliminary experience of video-mediastinoscopy in clinical application.
Jun WANG ; Hui ZHAO ; Jun LIU ; Jianfeng LI ; Yun LI
Chinese Journal of Surgery 2002;40(11):840-842
OBJECTIVETo determine the value of video-mediastinoscopy in clinical application.
METHODSThe clinical data of 54 patients receiving video-mediastinoscopy were reviewed retrospectively. This operation consisted of cervical mediastinoscopy in 44 patients, parasternal mediastinoscopy in 6, and combined procedures in 4. Of these patients, 18 underwent video-mediastinoscopy for the evaluation of undifferentiated mediastinal disease. Thirty-six patients with suspected lung cancer showed enlarged mediastinal lymph nodes radiographically in the chest and underwent video-mediastinoscopy.
RESULTSSeventeen of 18 patients with undetermined mediastinal diseases had a definitive pathologic diagnosis, with an accuracy of 94.4% (17/18). In the 36 patients with suspected lung cancer, 22 were positive, and 14 negative. In the negative patients who underwent thoracotomy with resection, mediastinal lymph nodes revealed no evidence of metastasis. There were no postoperative complication and deaths.
CONCLUSIONVideo-mediastinoscopy as a highly effective and safe procedure could be used in the diagnosis and staging of thoracic diseases.
Adolescent ; Adult ; Aged ; Female ; Humans ; Lung Neoplasms ; diagnosis ; Male ; Mediastinal Diseases ; diagnosis ; Mediastinoscopy ; Middle Aged ; Neoplasm Staging ; Thoracic Diseases ; diagnosis
7.Intradural Extramedullary Tuberculoma Mimicking En Plaque Meningioma.
Dae Moo SHIM ; Sung Kyun OH ; Tae Kyun KIM ; Soo Uk CHAE
Clinics in Orthopedic Surgery 2010;2(4):260-263
A 24-year-old man with tuberculosis meningitis developed acute paraplegia and sensory disturbances 5 weeks after receiving conventional antituberculous therapy. Magnetic resonance imaging revealed an intradural extramedullary long segmental mass mimicking en plaque meningioma at the T2-T6 vertebrae levels. Prompt surgical decompression was performed. A histology examination of the mass revealed a tuberculoma. After surgery, the patient showed improved motor power and a normal bladder function. Intradural extramedullary tuberculoma of the spinal cord is rare complication of tuberculosis meningitis, which can occur as a response to conventional antituberculous therapy.
Diagnosis, Differential
;
Humans
;
Male
;
Meningeal Neoplasms/*diagnosis
;
Meningioma/*diagnosis
;
Spinal Cord Diseases/*diagnosis/surgery
;
Thoracic Vertebrae
;
Tuberculoma/*diagnosis/surgery
;
Tuberculosis, Meningeal/*diagnosis/surgery
;
Young Adult
8.Intracardiac Echocardiography to Guide Biopsy for Two Cases of Intracardiac Masses.
Kwang In PARK ; Mi Joo KIM ; Jin Kyung OH ; Jae Hwan LEE ; Jae Hyeong PARK ; Si Wan CHOI ; Jin Ok JEONG ; In Whan SEONG
Korean Circulation Journal 2015;45(2):165-168
Pathologic diagnosis of a cardiac mass is vital in determining the proper treatment modality. Open heart surgery or transesophageal echocardiography guided biopsy can be feasible methods to confirm the pathology. However, the former is highly invasive and both methods require general anesthesia. The introduction of intracardiac echocardiography (ICE) can provide good anatomic information of heart and does not require general anesthesia. In this report, we present two cases of cardiac tumors which were confirmed by percutaneous biopsy under the guidance of an ICE. The patients underwent cardiac biopsy without any complications.
Anesthesia, General
;
Biopsy*
;
Diagnosis
;
Echocardiography*
;
Echocardiography, Transesophageal
;
Heart
;
Heart Neoplasms
;
Humans
;
Ice
;
Pathology
;
Thoracic Surgery
9.Low Grade Fibromyxoid Sarcoma in Chest Wall: One case report.
Gi Bok LEE ; Ki Woo HONG ; Hee Cheol PARK ; Won Jin LEE ; Kun Il KIM ; Kwang Min CHOI ; Hye Rim PARK ; Kee Taek JANG
The Korean Journal of Thoracic and Cardiovascular Surgery 2002;35(8):638-641
Low grade fibromyxoid sarcoma is a recently recognized, uncommon soft tissue neoplasm. It has a tendency to develop in deep soft tissue of young adults and a possibility of local recurrence or distant metastasis. Diagnostic criteria have not been well defined and this tumor has not been accepted as a distinct entity. Histologically, it is characterized by the presence of bland spindle cells with mainly whorled pattern of growth, set in alternating areas with a myxoid or fibrous stroma. Careful consideration of the morphological and immunohistochemical features of this tumor permit a positive diagnosis of low grade fibromyxoid sarcoma and allow its distinction from a number of other benign and malignant soft tissue neoplasms. We experienced a low grade fibromyxoid sarcoma in chest wall and report this case with a review of the literature.
Diagnosis
;
Humans
;
Neoplasm Metastasis
;
Recurrence
;
Sarcoma*
;
Soft Tissue Neoplasms
;
Thoracic Wall*
;
Thorax*
;
Young Adult
10.Giant Pericardial Lipoma as an Unusual Cause of Cardiomegaly.
Woo Jin KIM ; Kye Hun KIM ; Jae Yeong CHO ; Youngkeun AHN ; Myung Ho JEONG ; Jeong Gwan CHO ; Jong Chun PARK
Korean Journal of Medicine 2014;87(3):338-342
Cardiomegaly is a commonly encountered clinical presentation on simple chest radiographs, and it usually indicates the enlargement of one or more cardiac chambers. However, cardiomegaly less commonly comes from abnormalities in the structures adjacent to the heart, including pericardial effusion, enlarged great vessels, or mediastinal tumors. Pericardial lipoma is a rare primary cardiac tumor that can grow to a large size by the time of diagnosis and result in huge cardiomegaly because of a lack of symptoms. Here, we report a rare case of giant pericardial lipoma that presented as huge cardiomegaly on simple chest radiographs. Multi-modality cardiovascular imaging, including echocardiography and cardiac magnetic resonance imaging, played a key role in the diagnosis and development of a therapeutic treatment plan for the present case.
Cardiomegaly*
;
Diagnosis
;
Echocardiography
;
Heart
;
Heart Neoplasms
;
Lipoma*
;
Magnetic Resonance Imaging
;
Pericardial Effusion
;
Pericardium
;
Radiography, Thoracic