Congenital ectodermal dysplasia are a group of familial disorders that affect tissues and organs of ectodermal origin to varying degrees. It devided hidrotic type and anhidrotic type by geneologic origin and distinct clinical manifestationa. The hidrotic type usually trait by autosomal dominant gene and manifested dystrofic nails, defect of hair and eyebrow and palmoplantar hyperkeratosis. This patient is 16 year oId male. He had been dystrophic nails, alopecia since at birth, thereafter palmoplantar hyperkeratosis, clubbing fingers noted. C.R.C. Urinalysis, stool examination, chest x-ray were within normal limit. Biopsy specimen from palm revealed hyperkeratosis, hypergranulosis, acanthosis and, mild inflamrnatory cell infiltrate on upper dermis. Biopsy speeimen from the scalp revealed norrriaI findings except slight hypoplasia of ebaceaus gland.
Alopecia ; Biopsy ; Dermis ; Ectoderm ; Ectodermal Dysplasia* ; Eyebrows ; Fingers ; Genes, Dominant ; Hair ; Humans ; Male ; Parturition ; Scalp ; Thorax ; Urinalysis

No abstract available.
Depression* ; Prevalence*

No abstract available.

No abstract available.
Peutz-Jeghers Syndrome*

No abstract available.
Anemia, Hypoplastic, Congenital*

No abstract available.
Heterotaxy Syndrome*

Ants(Family Formicidae) are very successful organisms occuring in trernendous numbers worldwide in terrestrial habitats. All ant species may bite, and on species sting. 48 species in 26 genus have been reported in Korea, but only systemic reaction induced by the anti Brachyponera chinersis, has been reported in the Korea terature. A 48 year old man was stung on the neck, abdomen, and dorsum of the hand by flying stinging ants. He experienced moderate pain, burning and itching sensation. Clinical course and histopathologic findings of the lesions caused by the stinging ant was observed without specific treatment. The stinging ants collected from t,he patient.s skin and his house were identified as Euponera chosensis belonging to Subfamily Ponerinae. To the best of our know ledge, this is the first clinical repor of the insect sting by Euponera chosensis in the Korean literature.
Abdomen ; Ants ; Bites and Stings ; Burns ; Diptera ; Ecosystem ; Hand ; Humans ; Insect Bites and Stings* ; Insects* ; Korea ; Middle Aged ; Neck ; Pruritus ; Sensation ; Skin

The endoscopic variceal ligation(EVL) has been adopted as a new treatment for acute hemorrhage from esophageal varices that ranks the highest mortality rate in upper gastrointestinal tract bleedings. This treatment method has good effects for the urgent treatment and eradication of varices from acute variceal bleeding in repeated sessions. We enrolled 34 patients with an acute or chronic variceal bleeding episode at the time of admission in this study from Apr. 8, 1992 to June. 2, 1994. Among 34 patients, there were 31 males and 3 females, at ages between 45-66(mean: 52 years). The incidence of symptoms on admission was 10 in tarry stool, 9 in hematemesis 8 in ascites, 4 in hepatic encephalopathy and 3 in nonspecific symptoms. Varices were eradicated or reduced to grade I in 30(88.2%) of the 34 patients by 4-25 bands (mean: 10.8 bands) in 1-7 EVL sessions(mean: 3.1 sessions). After EVL, there are complicated by active bleeding in 3 patients, dysphagia in 3 patienta and transient chest discomfort in 5 patients but subsided during 24 hours. These results indicated that EVL is a safe method for treatment of bleeding from esophageal varices.
Ascites ; Deglutition Disorders ; Esophageal and Gastric Varices* ; Female ; Hematemesis ; Hemorrhage* ; Hepatic Encephalopathy ; Humans ; Incidence ; Ligation* ; Male ; Mortality ; Thorax ; Upper Gastrointestinal Tract ; Varicose Veins

No abstract available.
Thumb*

No abstract available.
Head*