No abstract available.
Hernia* ; Humans ; Infant, Newborn* ; Mothers*

The malignant fibrous histiocytoma (MFH) was first introduced in 1963 to refer to a group of soft-issue tumors characterized by a storiform or cartwheel-ike growth pattern and predominantly fibroblastic appearance. It was postulated that they were derived from histiocytes that could assume the appearance and function of fibroblasts. MFH has been recognized to be the most common sarcoma in the soft tissue of late adult life which involves the deep fascia or skeletal muscles of the extremities or retroperitoneum. It has been noted in other organs, however, it rarely arises in the liver. We report two cases of primary malignant fibrous histiocytoma of the liver histopathologically confirmed after surgical resection-storiform pleomorphic and myxoid subtypes in the 55 year old male and 49 year old female patients, respectively, and describes the clinical courses, characteristics and pathologic aspects with review of the related literatures.
Adult ; Extremities ; Fascia ; Female ; Fibroblasts ; Histiocytes ; Histiocytoma, Malignant Fibrous* ; Humans ; Liver* ; Male ; Middle Aged ; Muscle, Skeletal ; Sarcoma

No abstract available.
Heart Septal Defects, Atrial* ; Hemodynamics*

No abstract available.

No abstract available.
Porokeratosis

Purpose: Autologous osteochondral transplantation (AOT) is indicated for patients with a large osteochondral lesion of the talus (OLT), accompanying subchondral cyst, and the failure of bone marrow stimulation (BMS) procedures. Despite the many reports on the clinical results of surgical treatment for medial osteochondral lesions, those of lateral lesions are rare. This paper reports the intermediate-term clinical outcomes after AOT for lateral OLTs. Materials and Methods: Twenty-one patients with lateral OLTs were followed up for at least three years after AOT. The clinical evaluations comprised the Foot and Ankle Outcome Score (FAOS) and Foot and Ankle Ability Measure (FAAM). The radiographic assessment included the irregularity of the articular surface (subchondral plate), the progression of degenerative arthritis, and the changes in talar tilt angle and anterior talar translation. Results: The mean FAOS and FAAM scores improved significantly from 42.1 to 89.5 and 39.5 to 90.6 points, respectively, at the final follow-up (p<0.001). The radiological evaluation revealed two cases (9.5%) of articular step-off ≥2 mm and 1 case (4.8%) of progressive arthritis. The mean talar tilt angle and anterior talar translation improved significantly. As postoperative complications, there was one case of a local wound problem, one case of superficial peroneal nerve injury, and one case of donor site morbidity. At a mean follow-up of 62.3 months, no patient showed a recurrence of instability or required reoperation for OLT. Conclusion AOT for the lateral OLTs demonstrated satisfactory intermediate-term clinical outcomes, including daily and sports activity abilities. Most OLT could be accessed through lateral ligament division and capsulotomy, and the incidence of iatrogenic complications, such as recurrent sprains or chronic instability, was minimal. AOT appears to be an effective and relatively safe treatment for patients with large lateral osteochondral lesions unresponsive to conservative therapy, with subchondral cysts, or with failed primary BMS.

BACKGROUNDS: Hemodialysis remains the most important support for patients with end stage renal disease, and reliable vascular access is an essential component for their life. The internal arteriovenous fistula (AVF) fulfills nearly all of the criteria for an optimal access for chronic hemodialysis, such as long-term patency rate, low complication rate. OBJECTIVE: This retrospective study is to review our experience and to evaluate the patency rate and the influencing factors of graft failure of the AVF. MATERIAL AND METHODS: From May 1988 through January 1997, 251 fistulas were created of 243 patients in Chonbuk National University Hospital. Only 119 cases were able to follow up survey. The statistical analysis used by Chi-square and Kaplan-Meier method. RESULTS: The male versus female ratio was 1.3:1 and the age distribution was occurred on from 3rd decade to 7th decade (93%). The most common cause of renal failure was hypertension and diabetes (54 cases, 45.4%). Among the 119 cases, the autogenous graft fistulas were performed in 106 cases (wrist/snuff box/antecubital fossa, 94/7/5), PTFE graft fistulas were 13 cases. The autogenous graft failures were 28 cases (early/late 15/13), PTFE graft failures were 8 cases (early/late 5/3). Overall failures, the most common cause was thrombosis or stricture (41.6%), and then dysfunction, infection, dysperfusion, rupture, and aneurysm in order of frequency. Early failures were occurred in 20 patients (male/female, 15/5) and late failures in 16 patients (male/female, 3/13). Older age (over 50 years old) and PTFE graft were more higher failure rate than younger age and autogenous fistula. 12, 24, 36 months accumulated patency rates were 70, 62, 55%, retrospectively. CONCLUSIONS: The results suggest that early failure was more frequent in male, and late failure was more frequent in female. The significant influencing factors of graft failures were age and material, one is PTFE graft and the other is over 50 years old were higher failure rate.
Age Distribution ; Aneurysm ; Arteriovenous Fistula ; Constriction, Pathologic ; Female ; Fistula ; Follow-Up Studies ; Humans ; Hypertension ; Jeollabuk-do ; Kidney Failure, Chronic ; Male ; Middle Aged ; Polytetrafluoroethylene ; Renal Dialysis ; Renal Insufficiency ; Retrospective Studies ; Rupture ; Thrombosis ; Transplants

PURPOSE: Systemic lupus erythematosus(SLE) is a disease of immunologic origin, affecting multiple organs including joints, skin, kidneys, nervous system, heart and blood, with rare involvement of gut and liver. The incidence of renal disease in children with SLE was approximately 70 percent and tended to be more severe than in adults. Accordingly we have retrospectively studied on the prognostic indicators. METHODS: We investigated clinical manifestations, laboratory findings and renal biopsy findings of 14 cases of childhood lupus nephritis. RESULTS: A review of the clinical and pathological findings revealed as follows : male to female ratio was 1 : 6, immunologic laboratory findings showed, positive rates of anti-ds DNA antibody which was 57%, FANA 85%. The incidence of decreased C3 and C4 was 57%. The most common clinical features were fever(92%) and malar rash(21%). Renal biopsies were performed with the following results. There were 3 cases of mesangial proliferative glomerulonephritis, 1 case of focal and segmental proliferative glomerulonephritis, 9 cases of diffuse proliferative glomerulonephritis, and 1 of membranous glomerulonephritis. During the follow-up period, 3 patients with diffuse proliferative glomerulonephritis expired due to renal failure and pulmonary edema. CONCLUSION: When lupus nephritis is suspected, renal biopsy, tests for antinuclear antibody (ANA) and anti-ds-DNA, and complement profile should be performed. Early diagnosis and proper treatment can prevent rapid deterioration of renal function and improve long-term survival. Renal biopsy in lupus nephritis is of considerable value to both choice of therapy and predicting prognosis.
Adult ; Antibodies, Antinuclear ; Biopsy ; Child ; Complement System Proteins ; DNA ; Early Diagnosis ; Female ; Follow-Up Studies ; Glomerulonephritis ; Glomerulonephritis, Membranous ; Heart ; Humans ; Incidence ; Joints ; Kidney ; Liver ; Lupus Nephritis* ; Male ; Nervous System ; Prognosis ; Pulmonary Edema ; Renal Insufficiency ; Retrospective Studies ; Skin

One of surgical complications in cochlear implantation is the necrosis of the skin flap above the receiver-stimulator coil. We present a case of 55-year-old woman who underwent cochlear implantation and developed a bluish skin necrosis due to bone marking. The planned position for the receiver-stimulator was marked using methylene blue through skin to bone. She did not undergo skin flap thinning and underwent successful implantation with complete electrode insertion. Few weeks postoperatively, the patient developed bluish discoloration with progressive thick, blue eschar formation and skin flap necrosis. She subsequently underwent wound debridement and skin flap closure. Cochlear explantation was not necessary. Timely diagnosis and management about this complication is necessary to prevent further skin breakdown and subsequent device extrusion. This report identifies the marking using methylene blue as another possible source of skin flap necrosis in cochlear implantation, and surgeons should be aware of this potential complication.
Cochlear Implantation* ; Cochlear Implants* ; Debridement ; Diagnosis ; Electrodes ; Female ; Humans ; Methylene Blue* ; Middle Aged ; Necrosis* ; Postoperative Complications ; Skin* ; Wounds and Injuries

No abstract available.
Capillaries* ; Hemangioma, Capillary*