1.Lumbar Epidural Venography.
Jong Yeal PARK ; Kyu Ho LEE ; Hyung Keun KIM ; Sung Hoan HA ; Dal Su KIM
Journal of Korean Neurosurgical Society 1980;9(1):115-122
The clinical value of lumbar epidural venography(L.E.V.) has been stressed in diagnosing lumbar disc since Batson's desciption of vertebral venous system in 1940. We have tried this procedure by the selective catheterization of ascending lumbar and, or internal iliac vein to 16 patients with disc symptoms. In 6 patients with abnormal myelography, 4 revealed abnormal L.E.V. and in 2, the above procedure was failed. In 6 patients with disc-like symptoms but normal myelography, 2 were abnormal L.E.V., 2 normal and 2 failed. 3 with disc-like symptoms but equivocal myelography, abnormal L.E.V. was definitely shown in 2 patients and failed. Operation was done in 7 patients(6, abnormal myelography and one, only abnormal L.E.V.).
Catheterization
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Catheters
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Humans
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Iliac Vein
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Myelography
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Phlebography*
2.A Case of Hereditary Fructose Intolerance.
Eun Kyeong KANG ; Hye Ran YANG ; Jeong Kee SEO ; Sun Hoan BAI ; Joo Young JEONG ; Jae Sung KO ; Il Soo HA ; Jeong Han SONG ; Kyeong Ae WI ; Yoon Sook SHIN
Journal of the Korean Pediatric Society 2002;45(1):120-124
Hereditary fructose intolerance(HFI) is an autosomal recessive disease caused by catalytic deficiency of aldolase B in which affected homozygotes develop hypoglycemia and abdominal symptoms after taking foods containing fructose. Chronic exposure to fructose may lead to progressive hepatic injury, renal injury, growth retardation, and ultimately to liver and kidney failure. Herein, we report a case of HFI with presentation of episodic vomiting, diarrhea, cold sweating, abnormal liver function and failure to thrive after 12 months of her age. She developed an aversion to fruits and sweet-tasting foods. When she was admitted to hospital at the age of 30 months, hepatomegaly, and dysfunction of proximal renal tubule with renal tubular acidosis were noted. We confirmed the diagnosis via enzyme assay on biopsied liver and intestine. A fructose restrictied diet was recommended. The patient has been symptom free with normal liver functions since then.
Acidosis, Renal Tubular
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Diagnosis
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Diarrhea
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Diet
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Enzyme Assays
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Failure to Thrive
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Fructose
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Fructose Intolerance*
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Fructose-Bisphosphate Aldolase
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Fruit
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Hepatomegaly
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Homozygote
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Humans
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Hypoglycemia
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Intestines
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Kidney Tubules, Proximal
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Liver
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Renal Insufficiency
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Sweat
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Sweating
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Vomiting