No abstract available.
Granuloma, Pyogenic* ; Port-Wine Stain*

No abstract available.
Humans ; Inpatients*

The conversion of the ankylosed hip to a total hip arthroplasty may be indicated if a fused hip causes low back pain, pain in the ispilateral knee, or a fibrous ankylosis is painful. Fifteen hips converted to total hip arthroplasty between Aug., 1982 and Jul., 1988 have been reviewed one to seven years after operation and the results are as follows:1. Among the 15 hips, 8 cases confirmed as fibrous ankylosis and 7 cases confirmed as bony ankylosis. 2. The causes of ankylosis is as follow tuberculous arthritis(4 cases), secondary osteoarthritis due to pyogenic hip(4 cases), rheumatoid arthritis(4 cases), post-traumatic arthritis secondary to central fracture-dislocation of hip(2 cases), and ankylosing spondylitis(1 cases). 3. The duration of immobility of the involved hip ranged from two to twenty-five years. 4. In the 14 patients, three complained of low back pain, five of ipsilateral knee pain and six of ipsilateral hip pain. 5. The lower back pain due to malposition was relieved in all cases except ankylosing spondylitis, and the pain in ipsilateral knee was also relived in all cases after hip arthroplasty. 6. The average Harris score of the fifteen hips before arthroplasty and after was 50.1 and 88.1.
Ankylosis ; Arthritis ; Arthroplasty ; Arthroplasty, Replacement, Hip ; Hip ; Humans ; Knee ; Low Back Pain ; Osteoarthritis ; Spondylitis, Ankylosing

The Cronkhite-Canada syndrome is a rare, non-neoplastic, non-hereditary condition which consists of gastrointestinal polyposis associated with alopecia, onychodystrophy and hyperpigmentation of the skin. It usually encountered with severe diarrhea, weight loss and other malabsorption symptoms. The etiology of the condition is unknown. Usually, this syndrome is associated with a poor prognosis due to the effect of malabsorption and generalized debility. We report a case of this syndrome showing unusually rapid improvement after 3-month following only conservative treatment. To our knowledge, this is the first case report of Cronkhite-Canada syndrome in the Karean dermatologic literature.
Alopecia ; Diarrhea ; Hyperpigmentation ; Intestinal Polyposis* ; Prognosis ; Skin ; Weight Loss

No abstract available.
Child* ; Edema* ; Humans

Oculopharyngeal muscular dystrophy, one of the variants of chronic progressive external ophthalmoplegia, is a disorder characterized by progressive bilateral ptosis, immobility of the eyes and dysphagia. We have experienced a 46-year-old woman complaining of bilateral ptosis, mild dysphagia and immobility of the eyes. Oculopharyngeal muscular dystrophy was confirmed by clinical, electromyographic and histopathologic examination. Therefore, we report a case of oculopharyngeal muscular dystrophy with review of literatures.
Deglutition Disorders ; Female ; Humans ; Middle Aged ; Muscular Dystrophy, Oculopharyngeal* ; Ophthalmoplegia, Chronic Progressive External

Clinical observation about 34 infants of gestational diabetic mothers(IGDM) and 4 infants of overt diabetic mothers(IDM) was attempted on the 388 large infants(above 4kg.) among 9,263 neonates, who were delivered at the Ilshin Women's hospital during 19 months from Jan. 1977 to July 1978. Birth characteristics, maternal history and perinatal complications were compared with control group of non-diabetic mothers. The results were summerized as follows : 1. The frequency of large infants was 4.2%. Among the large infants, IGDM were 8.8% and IDM were 1.0%. 2. The mean birth weight of IGM ranging in gestational age from 38 to 44 weeks was 4,240gm. No relationship between gestational age and birth weight was noticed. 3. The clinical features of IGDM were asymptomatic hypoglycemia (14.7%), hyperbilir ubinemia(11.8%), Apgar score below 6 at 1min(8.8%), and cogenital mal-formations(5.9%)in order of frequency. But no remarkable difference was noticed between IGDM and control group. 4. Compared with control group, the incidence of gestational diabetic mothers with toxemia and complicated pregnancy was higher. But no diffenence was found about maternal history and other perinatal problems. 5. Among 4 cases of IDM, two with hyperbilirubinemia, Apgar score below 6 at 1 min. and asymptomatic hypoglycemia and one with congenital malformations were noted. One case expired with respiratory distress syndrome.
Apgar Score ; Birth Weight ; Gestational Age ; Humans ; Hyperbilirubinemia ; Hypoglycemia ; Immunoglobulin M ; Incidence ; Infant* ; Infant, Newborn ; Mothers* ; Parturition ; Pregnancy ; Toxemia

Amyloidosis is a disease complex associated with deposition of inscluble fibrillar protein in vnrious tissues of the body. Since the term, amyloidosis was first introduced by Virchow in 1853, there have been many reports in English literature, but only a few cases of iriinary systemic amyloidosis have been reported in Korea. A 56-year-old male was seven for facial purpuras, macroglossia, myilgia and arthralgia for 5 years. Histologically, the skin biopsy specimen showed amorphous, faintly eosinophilic and fissured masses of amyloid in the upper dermis that demonstrated characteristic green brefringence on Congo red staining when viewed under polarized light. Electron microscopic exanintion showed that nonbranching and nonanastomosing straigh. fibrils are irregularly arranged arouned tlie collagen fibers. Therefore, he was diagncsed with primary systemic amyloidsis by the characteristic clinical, histopathologic and ultrastructural findings.
Amyloid ; Amyloidosis* ; Arthralgia ; Biopsy ; Collagen ; Congo Red ; Dermis ; Eosinophils ; Humans ; Korea ; Macroglossia ; Male ; Middle Aged ; Purpura ; Skin

Sarcoidosis is a disease of unknown cause characterized by the presence of noncaseating granulomatous inflammation. Because the lungs and thoracic lymph nodes are almost always involved, most patients report acute or insidious respiratory problems. Although pulmonary manifestations are usually the major clinical concern in sarcoidosis, extrapulmonary involvement is common. We report a case of sarcoidosis of the axillary lymph nodes with no evidence of lung alteration.
Humans ; Inflammation ; Lung ; Lymph Nodes* ; Sarcoidosis*

A complex syndrome, later called as Prader-Willi syndrome, was first described in 1956 by Prader et al, and Zellweger and Schneider characterized this syndrome as hypogonadism, hypotonia, hypomentia and boesty. It is not rare in western countries and more than 400 cases have been reported until 1983. But our interest arose because of our recent experience of diffuse noncirrhotic fibrosis of the liver in a 6 year-old boy who had the clinical features of Prader-Willi syndrome. The core of liver showed destruction of most of the hepatic lobules, particularly of the acinar zone 3, and replacement bt diffuse fibrosis. The remaining liver cells underwent fatty change, and the overall changes resembled chronic sclerosing hyaline disease of the alcoholic type. Inflammation was negligible. This particular case suggests that the severe fatty change of liver could result in irreversible damage to the hepatocytes and progressive fibrosis.