No abstract available.
Sturge-Weber Syndrome*

No abstract available.
Sturge-Weber Syndrome*

No abstract available.
Sturge-Weber Syndrome*

Humans ; Infant, Newborn ; Sturge-Weber Syndrome

Adolescent ; Diagnosis, Differential ; Humans ; Male ; Sturge-Weber Syndrome ; pathology

PURPOSE: We reported the CT and MR findings of 2 cases with Sturge-Weber syndrome which were not accompanied by facial nevi. MATERIALS AND METHODS: They were examined with both CT and MR in one case and with MR only in the other case. RESULTS: CT was better than MR in the demonstration of the characteristic cortical calcification. MR was superior to CT in the depiction of the abnormalities of the surrounding parenchyma and the intense enhancement of pial angiomatosis with Gd-DTPA enhancement. CONCLUSION: Gd-DTPA enhanced MR imaging could be useful in the demonstration of the presence and extent of pial angiomatosis in patients with suspected Sturge-Weber syndrome.
Angiomatosis ; Gadolinium DTPA ; Humans ; Magnetic Resonance Imaging ; Nevus* ; Sturge-Weber Syndrome*

A case of Sturge-Weber Syndrome is presented in a male neonate with severe gangrenous ulcerative stomatitis involving the angiomatous skin lesion and leaving sequele of cleft lip and nasal disfiguration.
Cleft Lip* ; Congenital Abnormalities* ; Gingivitis, Necrotizing Ulcerative ; Humans ; Infant, Newborn ; Male ; Skin ; Sturge-Weber Syndrome*

Abdominal pseudocysts have been recorded infrequently as a complication of intraperitoneal shunting. Authors have experienced two cases of subphrenic pseudocyst as a complication of ventriculoperitoneal shunt, which were treated with revision of shunt. First patient had medulloblastoma with hydrocephalus. The other one was a patient who had subarachnoid hemorrhage and hydrocephalus from Struge Weber syndrome. It's diagnosis and treatment were discussed with review of literatures.
Brain Stem Infarctions ; Diagnosis ; Humans ; Hydrocephalus ; Medulloblastoma ; Sturge-Weber Syndrome ; Subarachnoid Hemorrhage ; Ventriculoperitoneal Shunt*

Sturge-Weber syndrome is a rare congenital anomaly which includes facial port-wine stains with ipsilateral intracranial, hemangioma, ipsilateral choroidal hemangioma, and congenital glaucoma. The syndrome is thought to result from dysmorphogenesis of cephalic neuroectoderm. We report a case of Sturge-Weber syndrome combined with congenital ocular anomaly such as phthisis bulbi, corneal opacity, and iris anomaly.
Choroid ; Corneal Opacity ; Glaucoma ; Hemangioma ; Iris ; Neural Plate ; Port-Wine Stain ; Sturge-Weber Syndrome*

We present a case of nevus flammeus associated with angiokeratoma of Fordyce and lymphangioma circumscriptum in a 26 year-old Korean man. We have known that the congenital hemangiomas may be associated with many syndromes such as Kasabacb-Merritt syndrome, Sturge-Weber syndrome and etc. Recently the congenital hemangiomas associated with angiokeratoma or lymphangioma were reported in several literatures, Watson and McCarthy reported that it seemed to be established that three types of benign vascular tumors had a common origin and grew in an identical fashion by projecting buds of endothelial tissue. So the congenital hemangiomas may have a close association with angiokeratoma or lymphangioma.
Adult ; Angiokeratoma* ; Hemangioma ; Humans ; Lymphangioma* ; Nevus* ; Port-Wine Stain* ; Sturge-Weber Syndrome