No abstract available.
Sturge-Weber Syndrome*

No abstract available.
Sturge-Weber Syndrome*

No abstract available.
Sturge-Weber Syndrome*

Humans ; Infant, Newborn ; Sturge-Weber Syndrome

Adolescent ; Diagnosis, Differential ; Humans ; Male ; Sturge-Weber Syndrome ; pathology

Sturge-Weber syndrome was rare. But reported from 1860. We present a typical case of Sturge-Weber syndrome in a child and discussed the symptoms, signs, and pathological finding of various examinations in neurosurgical field such as plain x-ray, 4-vessel angiography, CT scan, EEG, IQ test, exophthamometry, opthalmometry, and fundoscopy. We find marked abnormality and asymmetry in that examination.
Angiography ; Child ; Electroencephalography ; Humans ; Sturge-Weber Syndrome* ; Tomography, X-Ray Computed

Humans ; Infant ; Magnetic Resonance Imaging ; Male ; Sturge-Weber Syndrome ; diagnosis ; therapy ; Tomography, X-Ray Computed

Adult ; Female ; Humans ; Male ; Sturge-Weber Syndrome ; diagnosis ; pathology ; Young Adult

A trabeculectomy with mitomycin (0.2mg/ml, 5 minutes) was performed in a 28-year-old man with glaucoma associated with Sturge-Weber syndrome. Two prophylactic posterior sclerotomies were made in an attempt to prevent sudden uveal effusion. The surgery was uncomplicated. On the first postoperative day, however, the anterior chamber became shallow with hypotony (<4mmHg). A 360 degrees choroidal detachment with serous retinal detachment encroaching upon macula was recognized. On the third postoperative day, evacuation of the suprachoroidal space was performed. However, the eye remained hypotonus and choroidal expansion with overlying retinal detachment occured again. The bleb decreased in size with time and the intraocular pressures(IOPs) rose gradually (10-14mmHg). The choroidal and retinal detachment resolved spontaneously with the increased IOP in 40 days. Twenty seven monthes after trabeculectomy, he has a small localized. bleb. The IOP is maintained in the high-teens(15-20mmHg) without any medication.
Adult ; Anterior Chamber ; Blister ; Choroid ; Glaucoma* ; Humans ; Mitomycin ; Retinal Detachment* ; Retinaldehyde* ; Sturge-Weber Syndrome* ; Trabeculectomy*

PURPOSE: To observe MR findings of vascular abnormality in Sturge-Weber syndrome and to determine the value of MRI in diagnosis. MATERIALS AND METHODS: Ten patients with Sturge-Weber syndrome (age : 3 months-32 years)were evaluated by MR imaging ; in six and four cases, respectively, the results were correlated with those of CT and angiography. We retrospectively analysed changes in the cortical vein and deep venous system, including the medullary and subependymal vein, as well as an largement of the choroid plexus, leptomeningeal enhancement, and changes in diploic space. RESULTS: In all cases except one, in which non-contrast enhanced study had been performed, varying degrees of leptomeningeal enhancement were seen. In nine cases the cortical vein became smaller; enlargement of the choroid plexus was seen in eight cases, change in the diploic space in seven (including three in which there was angiomatous involvement), and enlargement of the deep venous system in seven. In younger patients, collateral pathways were less developed and leptomeningeal angiomatous changes were more pronounced than in those who were older. CONCLUSION: MRI is a useful modality for the evaluationn of vascular changes in Sturge-Weber syndrome. These changes vary according to a patient's age and the duration of the disease.
Angiography ; Choroid Plexus ; Diagnosis ; Humans ; Magnetic Resonance Imaging ; Retrospective Studies ; Sturge-Weber Syndrome* ; Veins