1.Mazabraud's Syndrome Coexisting with a Uterine Tumor Resembling an Ovarian Sex Cord Tumor (UTROSCT): a Case Report.
Cuneyt CALISIR ; Ulukan INAN ; Ulas Savas YAVAS ; Serap ISIKSOY ; Tamer KAYA
Korean Journal of Radiology 2007;8(5):438-442
The association of intramuscular myxoma and fibrous dysplasia is a rare disease known as Mazabraud's syndrome. We present a case of Mazabraud's syndrome coexisting with a uterine tumor and resembling an ovarian sex cord tumor (UTROSCT). This uterine tumor showed a high mitotic index and cytological atypia. To the best of our knowledge, the coexistence of the two different entities has not been reported in the literature.
Aged
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Biopsy
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Buttocks/pathology/surgery/ultrasonography
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Diagnosis, Differential
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Female
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Fibrous Dysplasia, Monostotic/complications/*diagnosis/surgery
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Humans
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Magnetic Resonance Imaging
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Myxoma/complications/*diagnosis/surgery
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Ovarian Neoplasms/*diagnosis
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Rare Diseases
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Sex Cord-Gonadal Stromal Tumors/*diagnosis
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Syndrome
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Uterine Neoplasms/complications/*diagnosis/surgery
2.Peutz-Jeghers syndrome complicated by cervical adenoma malignum and ovarian sex cord tumor with annular tubules: report of a case.
Chinese Journal of Pathology 2006;35(12):761-762
Adenocarcinoma
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complications
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metabolism
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pathology
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Adult
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Carcinoembryonic Antigen
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metabolism
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Diagnosis, Differential
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Female
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Humans
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Immunohistochemistry
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Ki-67 Antigen
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metabolism
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Ovarian Neoplasms
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complications
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metabolism
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pathology
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Peutz-Jeghers Syndrome
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complications
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metabolism
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pathology
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Proliferating Cell Nuclear Antigen
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metabolism
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Sex Cord-Gonadal Stromal Tumors
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complications
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metabolism
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pathology
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Uterine Cervical Neoplasms
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complications
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metabolism
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pathology
3.Refractory Hypertension and Isosexual Pseudoprecocious Puberty Associated with Renin-Secreting Ovarian Steroid Cell Tumor in a Girl.
Sun Hee LEE ; Mi Seon KANG ; Gyeong Sin LEE ; Woo Yeong CHUNG
Journal of Korean Medical Science 2011;26(6):836-838
Steroid cell tumor, not otherwise specified (NOS), are rare ovarian tumor, in addition, it is more rare in children. The majority of these tumors produce several steroid hormones, particularly testosterone. Estrogen also secreted by steroid cell tumor, NOS, but it is uncommon. Furthermore, hypertension is an infrequent sign in steroid cell tumor, NOS. An 8.5-yr-old girl with hypertension and frequent vaginal spotting visited at our clinic. On laboratory evaluation, secondary hypertension due to an elevated plasma renin level and isosexual pseudoprecocious puberty was diagnosed. Right solid ovarian mass was detected in radiologic tests. She underwent a right ooporectomy and it revealed renin and progesterone receptor positive steroid cell tumor, NOS. After operation, her blood pressure returned to normal level and vaginal bleeding disappeared. Even though this case is very rare, when hypertension coincides with virilization or feminization, a renin-secreting ovarian steroid cell tumor, NOS, should be considered.
Child
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Female
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Humans
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Hypertension/*etiology
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Ovarian Neoplasms/complications/*diagnosis/pathology
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Puberty, Precocious/enzymology/*etiology
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Receptors, Cell Surface/metabolism
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Receptors, Progesterone/metabolism
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Renin/blood
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Sex Cord-Gonadal Stromal Tumors/complications/*diagnosis/pathology
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Steroids/biosynthesis
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Tomography, X-Ray Computed
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Vacuolar Proton-Translocating ATPases/metabolism