No abstract available.
Chromosome Aberrations* ; Oncogenes*

Nasal dorsal suppor may be weakened or lost during the corrective rhinoplasty procedures such as resection of dorsal deviation, osteotomies and reposition of deviated nasal bones, and incision, fracture, resection or scoring of the dorsal septal strut especially in the small flat noses. Partial or total augmentation of the nasal dorsum has an important role in the correction of asymmetry and restoration of aesthetic balance in the considerable amount of traumatic nasal deformities. We reviewed medical records, pre- and postoperative photographs of 53 patients with traumatic nasal deformities, which had been corrected by augmentation rhinoplasties. The majority of the patients were male (70%), ages of twenties and thirties (79%), injection by automobile accident, fist blows, and sports activities (76%), and were operated more than 3 years after injury (74%). Types of deformities were deviation only (47%), depression only (23%), deviation and depression (19%), deviation and hump (8%), and depression and widening (6%). At least two corrective procedures were needed in the deviated deformities and one procedure in the depressed deformities. Materials for augmentation were silicone implants in 55% and autogenous tissues in 45%. In terms of postoperative complications, displacement and/or absorption were observed in 6 of 24 (25%) autogenous augmentations and displacement and/or swelling in 8 of 29 (27.6%) silicone augmentations.
Absorption ; Automobiles ; Congenital Abnormalities* ; Depression ; Humans ; Male ; Medical Records ; Nasal Bone ; Nose ; Osteotomy ; Postoperative Complications ; Rhinoplasty* ; Silicones ; Sports

No abstract available.
Dandy-Walker Syndrome*

No abstract available.
Child* ; Humans ; Neurilemmoma* ; Neurofibromatosis 1

OBJECTIVE: The purpose of this study is to evaluate clinical and radiological outcomes analysis of the laminoplasty in the elderly patients, and to compare with the non-elderly patients. METHODS: A retrospective study of the short term result in patients who had treated with the laminoplasty for cervical spondylotic myelopathy (CSM) was performed. From January 2008 to December 2012, total 62 patients were operated with single open-door technique because of CSM; 28 patients were the elderly and 34 patients were the non-elderly. We evaluated some factors including sex, symptom duration, estimated blood loss during operation, operation time, hospitalization day, complications, pre- and postoperative modified Japanese Orthopedic Association (mJOA) score, recovery rate of mJOA score, achieved mJOA score, mean cervical canal width and expansion ratio of antero-posterior diameter in order to identify difference between the two group. Clinical outcomes were calculated with the recovery rate of mJOA score at the time of one year after operation. RESULTS: Mean age were 71.9 in the elderly group and 52.9 in the non-elderly group. Although postoperative mJOA score in the elderly group was lower than that of the non-elderly group, achieved mJOA score was statistically same between the two groups. Other clinical and radiological outcomes were also statistically same. CONCLUSION: We conclude that the laminoplasty also assures good clinical outcomes in the elderly patients with CSM, same as in the non-elderly group.
Aged* ; Asian Continental Ancestry Group ; Hospitalization ; Humans ; Orthopedics ; Retrospective Studies ; Spinal Cord Diseases*

BACKGROUND: Lambert-Eton myasthenic syndrome(LEMS) is characterized by the clinical triad of muscle weakness, hyporeflexia, and autonomic dysfunction. In contrast to myasthenia gravis.LEMS is not commonly associated with respiratory failure. Any case of respiratory failure in LEMS has not been reported in Korea. CASE DESCRIPTION: The first case is a 61-tear-old male complained of proximal muscle weakness and dysarthria associated with severe dry mouth for 3 month and developed respiratory failure. The second case is a 65-tear-old male who began complaining of muscle weakness, weight loss, dry mouth, and recurrent respiratory difficulty for 14 months. Repetitive nerve stimulation(RNS) test for ulnar nerve showed CMAP with low amplitude, a significant decremental response at the low rate stimulation and a marked incremental response at the high rate stimulation in the left abductor digiti muscles in both cases. The first case had small cell carcinoma of the lung, but the second case presented with respiratory failure in the absence of malignancy. CONCLUSION:We experienced two cases of LEMS presenting respiratory failure. To our knowledge, this is the first report of respiratory failure in LEMS in Korea.
Carcinoma, Small Cell ; Dysarthria ; Humans ; Korea ; Lambert-Eaton Myasthenic Syndrome* ; Lung ; Male ; Mouth ; Muscle Weakness ; Muscles ; Reflex, Abnormal ; Respiratory Insufficiency* ; Ulnar Nerve ; Weight Loss

BACKGROUND: Lambert-Eton myasthenic syndrome(LEMS) is characterized by the clinical triad of muscle weakness, hyporeflexia, and autonomic dysfunction. In contrast to myasthenia gravis.LEMS is not commonly associated with respiratory failure. Any case of respiratory failure in LEMS has not been reported in Korea. CASE DESCRIPTION: The first case is a 61-tear-old male complained of proximal muscle weakness and dysarthria associated with severe dry mouth for 3 month and developed respiratory failure. The second case is a 65-tear-old male who began complaining of muscle weakness, weight loss, dry mouth, and recurrent respiratory difficulty for 14 months. Repetitive nerve stimulation(RNS) test for ulnar nerve showed CMAP with low amplitude, a significant decremental response at the low rate stimulation and a marked incremental response at the high rate stimulation in the left abductor digiti muscles in both cases. The first case had small cell carcinoma of the lung, but the second case presented with respiratory failure in the absence of malignancy. CONCLUSION:We experienced two cases of LEMS presenting respiratory failure. To our knowledge, this is the first report of respiratory failure in LEMS in Korea.
Carcinoma, Small Cell ; Dysarthria ; Humans ; Korea ; Lambert-Eaton Myasthenic Syndrome* ; Lung ; Male ; Mouth ; Muscle Weakness ; Muscles ; Reflex, Abnormal ; Respiratory Insufficiency* ; Ulnar Nerve ; Weight Loss

Cavernous malformations (CMs) arising from the optic nerve and chiasm are extremely rare. The authors present a case of 39-year-old woman with CMs of the optic chiasm. She was referred due to sudden onset of bitemporal hemianopsia and headache, the so-called 'chiasmal apoplexy'. MRI findings suggested a diagnosis of hemorrhage and vascular malformation of the optic chiasm. Pterional craniotomy revealed an intrachiasmatic cavernous malformation with hemorrhage. The malformation was totally excised, but field deficits remained unchanged after surgery.
Adult ; Caves ; Craniotomy ; Female ; Headache ; Hemianopsia ; Hemorrhage ; Humans ; Optic Chiasm ; Optic Nerve ; Stroke ; Vascular Malformations

The authors presented 9 cases of surgically treated CSF rhinorrhea, two of which were spontaneous and 7 were traumatic delayed. The duration of leakage was longer than 1 month in most cases and seven of the nine cases were complicated by meningitis. The leakage site was most accurately detected by metrizamide computed tomographic cisternography(MCTC) and the most frequent leakage site was the cribriform plate. Good surgical results were obtained by direct repair and/or shunt without recurrence during follow-up period from 7 months to 2 years.
Cerebrospinal Fluid Rhinorrhea ; Ethmoid Bone ; Follow-Up Studies ; Meningitis ; Metrizamide ; Recurrence

Neonatal lupus erythematosus (NLE) is an uncommon passive autoimmune disease in which there is a transplacental passage of anti-Ro or anti-La maternal autoantibodies. The cutaneous lupus lesions are commonly observed and usually resolve spontaneously. The cardiac involvement which sometimes needs the permanent pacemaker, however, is the most clinically significant manifestation of NLE. In addition, the hepatic and hematologic abnormalities are observed in approximately 10% of infants with NLE. Therefore, in the way of the evaluation of hematologic disorders in neonate, NLE should be included. We present a case of NLE in an infant born to a mother with anti-Ro, and he had skin rash, pancytopenia and mildly abnormal liver functions without cardiac manifestation.
Autoantibodies ; Autoimmune Diseases ; Exanthema ; Humans ; Infant ; Infant, Newborn ; Liver* ; Mothers ; Pancytopenia*