No abstract available.
Rhabdomyoma*

No abstract available.
Humans ; Infant, Newborn* ; Rhabdomyoma*

No abstract available.
Eye Movements ; Rhabdomyoma

No abstract available.
Humans ; Infant* ; Rhabdomyoma* ; Tetralogy of Fallot*

Humans ; Laryngeal Neoplasms ; Larynx ; Rhabdomyoma/diagnostic imaging*

The most common primary heart tumor in infants is the rhabdomyoma.It is known that tuberous sclerosis is found in half of the patients with cardiac rhabdomyoma. Because the prognosis of this tumor associated with subaortic stenosis is poor,the surgical intervention is indicated.We report one case of left ventricular rhabdomyoma with tuberous sclerosis.
Constriction, Pathologic ; Heart Neoplasms ; Humans ; Infant ; Prognosis ; Rhabdomyoma* ; Tuberous Sclerosis*

Symptomatic primary heart tumors are rare in newborn. Cardiac rhabdomyoma is the most common lesion of the primary heart tumors and over half of them are related to kthe tuberous s clerosis. We described a case of cardiac rhabdomyoma, in a 2 day-old female newborn who presented with dyspnea and cyanosis. A 2D Echocardiogram demonstrated two masses; one is in the rt. ventricle and another is in the interventricular septum. Additional cardiac masses and cerebral tubers and subependymal giant cell astrocytoma were found at autopsy.
Astrocytoma ; Autopsy ; Cyanosis ; Dyspnea ; Female ; Heart Neoplasms* ; Humans ; Infant, Newborn* ; Rhabdomyoma ; Tuberous Sclerosis*

Rhabdomyoma has been reported to be the most common type of cardiac tumors in fetuses and children, and multiple cardiac rhabdomyomas almost certainly signify the association with tuberous sclerosis. We report here on a case of Tetralogy of Fallot (ToF) that was associated with multiple rhabdomyomas and tuberous sclerosis. A two-year-old boy, who had undergone systemic-pulmonary shunt during the neonatal period, received total correction of his ToF after the complete regression of the cardiac tumor. The postoperative course was uneventful, and he has been follow-up for 2 months. The boy is currently in an excellent condition.
Child ; Fetus ; Follow-Up Studies ; Heart Neoplasms ; Humans ; Rhabdomyoma ; Tetralogy of Fallot ; Tuberous Sclerosis

Primary cardiac tumors in infancy and childhood are rare, with fibromas being the second most common tumor after rhabdomyomas. Although cardiac fibromas are characteristically benign intramural tumors, they may exhibit expansile growth resulting in obstruction, valvular dysfunction, as well as other problems so early diagnosis and successful surgical excision are important. We experienced a case of cardiac fibroma in right ventricle that diagnosed by transthoracic echocardiography, chest CT, open heart tissue biopsy etc.
Biopsy ; Early Diagnosis ; Echocardiography ; Fibroma* ; Heart ; Heart Neoplasms ; Heart Ventricles ; Rhabdomyoma ; Tomography, X-Ray Computed

Orbital rhabdomyoma is an exceedingly rare, benign, slow growing tumor of mature myofibers. The authors experienced a case of orbital rhabdomyoma in three-year old female who had limitation of eyeball movement with marked proptosis of the left eye. The subtotal orbital exenteration with preservation of lid, conjunctiva, cornea, and sclera through lateral orbitotomy was performed. The removed tumor was consisted of many irregularly shaped fragments of grayish tan soft tissue, me as uring 0.7 X 1.8 X 1.0 cm in size. Pathologically it was proved as orbital rhabdomoma as seen in adult. Postoperatively the conjunctival sac was well preserved and artificial eye could be successfully fitted.
Adult ; Conjunctiva* ; Cornea* ; Exophthalmos ; Eye, Artificial ; Female ; Humans ; Orbit* ; Rhabdomyoma* ; Sclera* ; Triacetoneamine-N-Oxyl