This study presents a series of patients with Hirschsprung's disease (HD) who underwent a one-stage endorectal pull-through procedure using a purely transanal approach. A total of11 patients, 7(64%) males and 4(36'10) females, with a mean age of 2.37 years underwent the procedure over an IS-month period. Mean operating time was 108 minutes. The average length of bowel resected was 17.32 ern, which correlated well with the barium enema transition zone. No patient required conversion to open procedure. The mean total hospital stay was 5 days. Postoperatively, two patients developed enterocolitis that responded to conservative management.Follow up ranged from 4 to 14 months. No deaths occurred in this series. This procedure can be performed successfully in patients with short segment HD. This technique is associated with good clinical results and no visible scars.

Human ; Male ; Female ; Barium Enema ; Conservative Treatment ; Cicatrix ; Hirschsprung Disease ; Enterocolitis ; Digestive System Surgical Procedures ; Rectum

Presented is a rare case of Wilms' Tumor (WT) in a 3-month old female with a palpable nontender left flank mass. In the early infancy period (<6 months), there is a low incidence of malignancy in renal masses, and congenital benign renal lesions (like congenital mesoblastic nephroma) predominate in this age group. We did nephroureterectomy and lymph node sampling. Histopathology revealed localized non-metastatic COG Stage I WT with favorable histologic features. The patient underwent adjuvant chemotherapy with dactinomycin and vincristine using an institution based protocol, which offers upfront surgery followed by chemotherapy. This approach is similar to the Children's Oncology Group (COG) protocol.
Nephrectomy