1.A case of protein losing enteropathy diagnosed by alpha 1 antitryp-sin clearance.
Baek Soo KIM ; Kyung Soon SONG ; Hoon Sang CHI ; Kyung Hi KIM
Korean Journal of Clinical Pathology 1991;11(2):369-373
No abstract available.
Protein-Losing Enteropathies*
2.A case of intestinal lymphangiectasia.
Yae Kyung SUH ; Kyung Hee PARK ; Chul Ho JANG ; Bum Soo PARK ; Jeong Kee SEO ; Sung Hae PARK ; Je Geun CHI ; Kyung Mo YEON ; Kwi Won PARK
Journal of the Korean Pediatric Society 1992;35(12):1737-1743
No abstract available.
Protein-Losing Enteropathies
3.Bilateral Central Serous Retinal Detachment in Protein-losing Enteropathy
Mostafa MAFI ; Alireza KHODABANDEH ; Hamid RIAZI-ESFAHANI ; Masoud MIRGHORBANI
Korean Journal of Ophthalmology 2019;33(6):577-578
No abstract available.
Protein-Losing Enteropathies
;
Retinal Detachment
;
Retinaldehyde
4.Treatment of Protein-losing Enteropathy After Fontan Procedure by Conversion to the Total Cavopulmonary Connection with Fenestration.
Hyun Sung LEE ; Young Hwan PARK ; Yoo Sun HONG ; Seok Won SONG ; Jin Goo LEE ; Bum Koo CHO
The Korean Journal of Thoracic and Cardiovascular Surgery 2001;34(1):85-90
As the operative mortality has diminished and the number of survivors has increased after Fontan procedure, morbidities related to the unnatural physiology of cavopulmonary flow have developed. One of the complications by the hemodynamic derangement after Fontan procedure is a protein-losing enteropathy. This is a rare but life-threatening complication after the Fontan operation. Treatment strategies are highly variable. But, reports on successful management are limited. We experienced three cases of protein-losing enteropathy after the Fontan operation. We report that the conversion to the total extracardiac or intracardiac cavopulmonary connection with fenestration is a satisfactory treatment modality for protein- losing enteropathy after the Fontan operation.
Fontan Procedure*
;
Hemodynamics
;
Humans
;
Mortality
;
Physiology
;
Protein-Losing Enteropathies*
;
Survivors
5.A Case of Protein-Losing Enteropathy Associated with Systemic Lupus Erythematosus.
Chang Ok YOON ; Tae Hwan KIM ; Mun Su KANG ; Jeong Ik LEE ; Tae Young KANG ; Ki Chan KIM ; Young Cheol JUN ; Sung Soo JUNG ; In Hong LEE ; Yong Wook PARK ; Seong Yoon KIM
The Journal of the Korean Rheumatism Association 2001;8(1):48-52
Systemic lupus erythematosus (SLE) is a multisystemic disease that can affect most organ system, although gastrointestinal (GI) manifestations are relatively uncommon. Protein losing enteropathy (PLE) is associated with several clinical disorders, but it is an unusual manifestation of SLE. Of over 20 reported cases of PLE associated with SLE, the pathogenesis of lupus associated PLE remains unclear. We describe a patient with edema, diarrhea, abdomianl pain, and hypoalbuminemia who had been diagnosed SLE. PLE was diagnosed by the method of alpha1-antitrypsin clearance in stool.
Diarrhea
;
Edema
;
Humans
;
Hypoalbuminemia
;
Lupus Erythematosus, Systemic*
;
Protein-Losing Enteropathies*
6.A case of systemic lupus erythematosus with chylothorax, chronic interstitial cystitis and protein-losing enteropathy.
Kung No LEE ; Young Hwan PARK ; Seung Hwan LEE ; Jae Chun LEE ; Mi Kyoung LIM ; You Sook CHO ; Bin YOU ; Hee Bom MOON
Korean Journal of Medicine 2000;59(5):555-560
Systemic lupus erythematosus(SLE) is the prototypic immune complex disease which involves various organs. Chronic interstitial cystitis and protein-losing enteropathy are uncommon manifestations of SLE and have good response to steroid. Only one case of SLE associated with chronic interstitial cystitis and protein-losing enteropathy has been reported which was resistant to steroid treatment but dramatically responded to cyclophosphamide. We describe a case of a female patient who developed systemic lupus erythematosus associated with chylothorax, interstitial cystitis and protein-losing enteropathy with literature review. This case was initially resistant to steroid but with the addition of cyclophosphamide, chylothorax, chronic interstitial cystitis and protein-losing enteropathy markedly improved. This is the first case of SLE that developed chylothorax as well as chronic interstitial cystitis and protein-losing enteropathy.
Chylothorax*
;
Cyclophosphamide
;
Cystitis, Interstitial*
;
Female
;
Humans
;
Immune Complex Diseases
;
Lupus Erythematosus, Systemic*
;
Protein-Losing Enteropathies*
7.A Systemic Lupus Erythematosus Patient with Protein Losing Enteropathy.
Jee Min PARK ; Sun Young AHN ; Jae Il SHIN ; Mi Jin YUN ; Jae Seung LEE
Yonsei Medical Journal 2004;45(5):923-926
Protein-losing enteropathy (PLE) is a rare manifestation of systemic lupus erythematosus (SLE), and it is an uncommon cause of hypoalbuminemia without proteinuria. We describe a case of an 11 year-old girl who had diarrhea and periorbital edema as the initial symptoms of SLE. PLE was diagnosed by 24-hour stool alpha-1 antitrypsin clearance and 99mTc-human serum albumin scintigraphy.
Child
;
Female
;
Humans
;
Lupus Erythematosus, Systemic/*complications
;
Protein-Losing Enteropathies/*etiology
8.A case of constrictive pericarditis presenting with protein-losing enteropathy.
Jeong Mi HONG ; Jae Young LEE ; Soo Jin KIM ; Gi Young JANG ; Woo Sup SHIM
Korean Journal of Pediatrics 2006;49(8):898-901
Constrictive pericarditis represents a rare cause of protein-losing enteropathy in children. Reported is an 11-year-old girl with protein-losing enteropathy (PLE) as the principal manifestations of constrictive pericarditis. After total pericardiectomy, symptoms and signs of PLE disappeared. Doppler echocardiography including tissue Doppler imaging is a useful noninvasive initial diagnostic tool for differential diagnosis of diastolic heart failure.
Child
;
Diagnosis, Differential
;
Echocardiography, Doppler
;
Female
;
Heart Failure, Diastolic
;
Humans
;
Pericardiectomy
;
Pericarditis, Constrictive*
;
Protein-Losing Enteropathies*
9.A Case of Primary Intestinal Lymphangiectasia Diagnosed by Double Balloon Enteroscopy.
Jung Min LEE ; Jong Bum KIM ; Seung Wook BAK ; Bong Kyu LEE ; Nam Hun LEE ; Young Ho SEO
Intestinal Research 2013;11(1):66-70
Primary intestinal lymphangiectasia is a congenital lymphatic disorder characterized by dilated intestinal lacteals resulting in lymph leakage into the small bowel lumen and responsible for protein losing enteropathy. As a result, generalized edema, hypoalbuminemia, and lymphocytopenia are clinically manifested. We could not find the reason by several examinations. Therefore, we performed double balloon enteroscopy (DBE), and intestnal lymphangiectasia was diagnosed histologically by a biopsy. DBE is a safe and effective method to diagnose small bowel lymphangiectasia. We report a case of primary intestinal lymphangiectasia, which occurred in a 54-year-old male patient with generalized edema and ascites.
Ascites
;
Biopsy
;
Double-Balloon Enteroscopy
;
Edema
;
Humans
;
Hypoalbuminemia
;
Lymphopenia
;
Male
;
Protein-Losing Enteropathies
10.A Case of Primary Intestinal Lymphangiectasia.
Dae Hwan HWANG ; Jung Woo HAN ; Ji Hong KIM ; Seok Joo HAN ; Soon Won HONG
Korean Journal of Pediatric Gastroenterology and Nutrition 2004;7(2):253-259
Primary intestinal lymphangiectasia is a congenital lymphatic disorder in which intestinal lymphatic channels are dilated and ruptured resulting in loss of protein, lipid, and lymphocyte into the intestine or peritoneum. As a result, hypoalbuminemia, generalized edema, diarrhea are clinically manifested. We report a case of primary intestinal lymphangiectasia with generalized edema which occurred in a 7-year old boy who was treated with lipid restriction diet with medium chain triglyceride oil supplement.
Child
;
Diarrhea
;
Diet
;
Edema
;
Humans
;
Hypoalbuminemia
;
Intestines
;
Lymphocytes
;
Male
;
Peritoneum
;
Protein-Losing Enteropathies
;
Triglycerides