1.A case of acute intermittent porphyria in pregnancy.
Woo Hyun CHANG ; Hyun Soo CHUNG ; Jong Woo SOHN ; Young Ho KOH ; Jin Ki HONG ; Byung Hee SUH
Korean Journal of Obstetrics and Gynecology 1993;36(7):2435-2440
No abstract available.
Porphyria, Acute Intermittent*
;
Pregnancy*
2.A Case of Acute Intermittent Porphyria in Pregnancy.
Young Mi SUNG ; Bong Ho KOH ; Ji Sung LEE ; Ji Hong PARK
Korean Journal of Obstetrics and Gynecology 1997;40(12):2913-2917
No abstract available.
Porphyria, Acute Intermittent*
;
Pregnancy*
3.Acute Intermittent Porphyria Presenting with Periodic Leg Pain.
Hye Jin LEE ; Soojeong KIM ; Jeeyoung OH
Journal of the Korean Neurological Association 2017;35(1):53-54
No abstract available.
Leg*
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Porphyria, Acute Intermittent*
;
Porphyrias
4.Acute Intermittent Porphyria and Pregnancy.
Ji Hee RYU ; Eun A CHOI ; Hyung Min CHOI ; Tae Yoon KIM ; Jae Sung CHO ; Yong Won PARK ; Jae Wook KIM
Korean Journal of Obstetrics and Gynecology 1997;40(2):414-418
The Porphyria are a group of inherited and acquired disorders characterized by partial defects in the heme biosynthetic pathway. Among the hepatic forms, acute intermittent porphyria(AIP) is the most severe and common type in western hemisphere. Though its association with pregnancy is rare, it presents the obstetrician with challenging problems in diagnosis and management and it is probable that pregnancy had some deleterious effect in acute porphyria. The authors present a cae of AIP in pregnancy with a review of literature.
Biosynthetic Pathways
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Diagnosis
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Heme
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Porphyria, Acute Intermittent*
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Porphyrias
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Pregnancy*
6.A Case of Acute Intermittent Porphyria: A case report.
Chang Heon YANG ; Moon Kwan CHUNG ; Hyun Woo LEE
Yeungnam University Journal of Medicine 1989;6(1):205-211
We report a case of acute intermittent porphyria presenting with variable symptoms and signs such as hypertension, polyneuropathy, syndrome of inappropriate secretion of antidiuretic hormone and cerebral infarction. A 47 year-old female patient entered hospital with abdominal pain followed by generalized seizure. She was diagnosed to have acute intermittent porphyria in consequence of Watson-Schwartz test and δ-ALA in 24 hours urine. She was managed with conservative treatment but died of respiratory failure.
Abdominal Pain
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Cerebral Infarction
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Female
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Humans
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Hypertension
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Polyneuropathies
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Porphyria, Acute Intermittent*
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Respiratory Insufficiency
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Seizures
8.Acute Intermittent Porphyria: A Diagnostic Challenge for Endocrinologist.
Tao YUAN ; Yu-Hui LI ; Xi WANG ; Feng-Ying GONG ; Xue-Yan WU ; Yong FU ; Wei-Gang ZHAO
Chinese Medical Journal 2015;128(14):1980-1981
9.One case of acute intermittent porphyria.
Ping ZHOU ; Zhi-min REN ; Qiang GAO
Chinese Journal of Pediatrics 2004;42(7):531-531
10.Research Progress in Pathogenesis of Hypertension in Acute Intermittent Porphyria.
Qing-Yang LI ; Yi REN ; Jian-Hong WANG ; Jing YANG
Acta Academiae Medicinae Sinicae 2023;45(1):129-133
Acute intermittent porphyria (AIP) has complicated clinical manifestations and is often accompanied by hypertension.AIP may cause hypertension through adrenergic effect,heme deficiency,inflammation,inappropriate secretion of antidiuretic hormone,toxicity of delta-aminolevulinic acid(ALA,aporphyrin precursor),and elevated serum glucose level.The prevention and treatment strategies for AIP accompanied with hypertension mainly include the controlling of porphyria attacks,application of antihypertensive drugs,lifestyle intervention,and management of latent AIP patients.
Humans
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Porphyria, Acute Intermittent
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Blood Glucose
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Hypertension/etiology*
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Inflammation
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Life Style