No abstract available.
Pityriasis Rubra Pilaris* ; Pityriasis*

No abstract available.
Cyclosporine* ; Pityriasis Rubra Pilaris* ; Pityriasis*

No abstract available.
Pityriasis Rubra Pilaris ; Pityriasis ; Ustekinumab

No abstract available.
Acrodermatitis* ; Adult* ; Humans ; Pityriasis Rubra Pilaris* ; Pityriasis* ; Zinc*

No abstract available.
Humans ; Keratoderma, Palmoplantar ; Pityriasis Rubra Pilaris ; Pityriasis ; Siblings

Pityriasis Rubra Pilaris is a rare, chronic, mildly inflammatory disease characterized by fine acuminate follicular papules with orange-red to salmon-colored scaling of the skin and erythroderma that surround islands of normal, uninvolved skin, particular in the trunk. Most patients also develop palmoplantar hyperkeratosis in the early course of the disease. Focal acantholysis occurring in pityriasis rubra pilaris is an unusual and incidental histologic finding within the spectrum of histologic change of the disease. No case featuring this concomitant histologic finding has been reported in the Korean literatures up to date. We report a case of focal acantholysis occurring in a patient with the clinical features of pityriasis rubra pilaris which may be considered as an incidental finding.
Acantholysis* ; Dermatitis, Exfoliative ; Humans ; Incidental Findings ; Islands ; Pityriasis Rubra Pilaris* ; Pityriasis* ; Skin

BACKGROUND: Pityriasis rubra pilaris (PRP) is a rare disease characterized by widespread follicular acuminate papules. Traditionally, two forms have been described : hereditary (juvenile) and acquired (generally aduIrt). A.substantial contribution, however, suggests that further subdivision is appropriate. OBJECTIVE: The purpose of this study was to investigate clinicopathologic features of PRP and to compare the results of clinical classification with Griffiths' classification. METHODS: The retrospective clinicopathologic study carried out in 30 cases of PRP over the last 30 years. RESULTS: 1. The incidence of type lV was 38.5%. For both type I and III it was 30.8%. The onset ages of the type I, III, and lV were 36.1, 6.0, and 96 years respectively. 2. The most common site of initial involvement was the palms, and the most common involvement site during the diease course was the dorsa of palms and feet. The incidence involved in the whole body was 46.6%. 3. The incidences of insidious and acute onset were 60% and 40% respectively. No case had the family history of PRP. 4. In the histopathologic study, diffuse hyperkeratosis, acanthosis, and mild dermal infiltrations were found in all cases. Follicular pluggings were observed in 93.3% of cases CONCLUSION: We investigated the clinical classifications and clinicopathologic features of PRP. We think that more studies such as prognosis and treatment of PRP should be achieved in the near future.
Classification ; Foot ; Humans ; Incidence ; Pityriasis Rubra Pilaris* ; Pityriasis* ; Prognosis ; Rare Diseases ; Retrospective Studies

Acantholytic dyskeratosis is seen in Darier's disease, transient acantholytic dermatosis and warty dyskeratoma. It is also occasionally observed incidental histological finding in pityriasis rosea, pityriasis rubra pilaris and is occasionally found in linear epidermal nevus. A 10-month-old boy presented linear hyperkeratotic plaques on the right sole and the left hand along with erythematous scaly papules on the posterior neck, the left axilla and the face. Histological findings showed acantholytic dyskeratosis with common histopathological findings of epidermal nevus. Acantholytic dyskeratosis is an occasional finding in linear epidermal nevus, but has been rarely reported in an infant(5 cases reported in 20 years). We report a case of linear epidermal nevus with acantholytic dyskeratosis in an infant.
Axilla ; Darier Disease* ; Hand ; Humans ; Infant ; Male ; Neck ; Nevus ; Pityriasis Rosea ; Pityriasis Rubra Pilaris ; Skin Diseases

We report herein a case of pityriasis rubra pilaris in a 39-year-old male, who had erythematous scaly patches on the face, trunk and extremities for one year. The skin lesion showed well defined plaques on the elbow and knee joint areas, and exfoliative hyperkeratotic sheets with fissures on the palms and soles. He had no family and past history of such skin lesion. He was treated with etretinate lmg/kg/day for 1 week initially, and then tapered off 0.5mg/kg/day for 5 weeks with marked improvement. There was no exacerbation and recurrence of the skin lesion for about 1 year.
Acitretin* ; Adult ; Elbow ; Etretinate* ; Extremities ; Humans ; Knee Joint ; Male ; Pityriasis Rubra Pilaris* ; Pityriasis* ; Recurrence ; Skin

The Koebner phenomenon is the development of the isomorphic skin lesions in persons with certain skin diseases after an injury occurred on normal-appearing skin. This response can be developed in psoriasis, pityriasis rubra pilaris, verruca etc. Several types of injury can produce the Koebner phenomenon such as irritation, physical injury, surgical wound, and sunburn or radiation therapy. We report a case of psoriasis developed by Koebner phenomenon after radiation therapy and this is the first report in Korea.
Humans ; Intraoperative Complications ; Korea ; Pityriasis Rubra Pilaris ; Psoriasis* ; Skin ; Skin Diseases ; Sunburn ; Warts ; Wounds and Injuries